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妊娠期抗γ-氨基丁酸B(GABA B)抗体受体相关自身免疫性脑炎:一种罕见疾病。

Anti-Gamma Aminobutyric Acid B (GABA B) Antibody Receptor-Associated Autoimmune Encephalitis in Pregnancy: A Rare Condition.

作者信息

Mazumdar Md Aziz, Bansal Sonali, Shukla Isha

机构信息

Medicine, Park Hospital, Gurgaon, IND.

Critical Care Medicine, Park Hospital, Gurgaon, IND.

出版信息

Cureus. 2024 Nov 11;16(11):e73494. doi: 10.7759/cureus.73494. eCollection 2024 Nov.

Abstract

We report a primigravida 31-year-old female patient hospitalized at 32 gestational weeks with status epilepticus. In due course of illness, she developed refractory status epilepticus managed with induced coma with propofol and emergency early lower section caesarean surgery (LSCS). A battery of initial laboratory and radiological tests did not lead to a definite diagnosis. On further workup, she was diagnosed with anti-gamma aminobutyric acid B (GABA B) receptor autoimmune encephalitis that responded to immunotherapy and pulse steroids.

摘要

我们报告了一名31岁的初产妇,在孕32周时因癫痫持续状态入院。在病程中,她发展为难治性癫痫持续状态,采用丙泊酚诱导昏迷和急诊早期低位剖宫产手术(LSCS)进行治疗。一系列初步实验室和影像学检查未得出明确诊断。进一步检查后,她被诊断为抗γ-氨基丁酸B(GABA B)受体自身免疫性脑炎,对免疫治疗和冲击性类固醇治疗有反应。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c47d/11635330/fd00493be519/cureus-0016-00000073494-i01.jpg

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