de Souza Andrade J, Bambirra E A, Bicalho O J, de Souza A F
J Urol. 1985 Feb;133(2):288-9. doi: 10.1016/s0022-5347(17)48920-8.
We report a case of bilateral papillary cystadenoma of the epididymis thought to be a component of the von Hippel-Lindau syndrome. The patient was hospitalized initially because of infertility. He had undergone a craniotomy 2 years previously for the diagnosis of a cerebellar hemangioblastoma. Funduscopy had revealed angiomatous lesions of the left eye. The von Hippel-Lindau syndrome is discussed briefly and the importance of long-term urological followup for possible presentation of silent renal carcinoma is emphasized. Patients with bilateral epididymal papillary cystadenoma are prone to have other components of the von Hippel-Lindau syndrome, and clinical studies are indicated in all such patients.
我们报告一例双侧附睾乳头状囊腺瘤，考虑为冯·希佩尔-林道综合征的一部分。患者最初因不育症住院。他在两年前因诊断为小脑成血管细胞瘤而接受了开颅手术。眼底检查发现左眼有血管瘤样病变。简要讨论了冯·希佩尔-林道综合征，并强调了长期进行泌尿外科随访以发现可能隐匿性肾癌的重要性。双侧附睾乳头状囊腺瘤患者易患冯·希佩尔-林道综合征的其他病变，所有此类患者均需进行临床研究。
