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伴有多发性颅神经病变、脑膜炎及随后脑干脑炎的拉姆齐·亨特综合征:一例报告

Ramsay Hunt Syndrome With Multiple Cranial Neuropathies, Meningitis, and Subsequent Brainstem Encephalitis: A Case Report.

作者信息

Kawamoto Satoshi, Yoshinaga Kazuhiro, Watanabe Ryosuke, Hirano Takashi

机构信息

Otolaryngology, Oita University, Yufu, JPN.

Neurology, Oita University, Yufu, JPN.

出版信息

Cureus. 2024 Nov 17;16(11):e73861. doi: 10.7759/cureus.73861. eCollection 2024 Nov.

DOI:10.7759/cureus.73861
PMID:39691149
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11651707/
Abstract

We present a case of Ramsay Hunt syndrome in a previously healthy 49-year-old male, complicated by ipsilateral glossopharyngeal, vagus, accessory, and hypoglossal nerve palsies, along with meningitis. Despite a course of antiviral therapy and steroids for meningitis, the patient experienced a relapse, developing varicella-zoster virus (VZV) brainstem encephalitis after an initial period of stability. Hunt syndrome can be encountered in otolaryngology and internal medicine, dermatology, and other specialties. We report a case of Ramsay Hunt syndrome complicated by multiple cranial neuropathies and Hunt syndrome-associated meningitis and encephalitis, accompanied by a literature review.

摘要

我们报告一例49岁既往健康男性的拉姆齐·亨特综合征,该病例并发同侧舌咽神经、迷走神经、副神经和舌下神经麻痹以及脑膜炎。尽管接受了针对脑膜炎的抗病毒治疗和类固醇治疗,但患者仍复发,在初始稳定期后发生了水痘-带状疱疹病毒(VZV)脑干脑炎。亨特综合征可见于耳鼻喉科、内科、皮肤科及其他专科。我们报告一例并发多发性颅神经病变以及亨特综合征相关脑膜炎和脑炎的拉姆齐·亨特综合征病例,并伴有文献综述。

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