Fuentes-Calvo Irving, Gomez-Oropeza Irene, Hernandez-Carrasco Adriana, Martinez Medina Salvador
Neurology, National Institute of Neurology and Neurosurgery "Dr. Manuel Velasco Suárez", Mexico City, MEX.
Cureus. 2024 Nov 22;16(11):e74259. doi: 10.7759/cureus.74259. eCollection 2024 Nov.
Anti-N-methyl-D-aspartate receptor (NMDAR) encephalitis stands as the most prevalent form of autoimmune encephalitis, primarily affecting young patients and exhibiting a higher incidence among females. Patients frequently present with psychiatric symptoms or cognitive impairments such as speech disturbances, decreased level of consciousness, autonomic dysfunction, as well as seizures, dyskinesias, and catatonia due to overactivation of extrasynaptic NMDA receptors. To date, there is no gold standard for the diagnosis of catatonia; however, a few rating scales exist to measure this phenomenon, with the Bush Francis Catatonia Rating Scale being the most commonly used due to its validity, reliability, and ease of application. In this case, we present a 19-year-old female who experienced onset symptoms including fluctuating headaches, dysthymia, tinnitus, and prosopagnosia. Eventually, she experienced spatial disorientation and hypoesthesia in the left hemiface, along with insomnia. Subsequently, she reported alterations in perception, accompanied by urinary and fecal incontinence. Upon admission, the patient presented as catatonic. The lumbar puncture revealed normal cell counts, proteins, and glucose levels, along with the presence of reactive anti-NMDAR antibodies in serum and electroencephalogram findings indicating generalized dysfunction, meeting Graus criteria for probable encephalitis. A CT scan revealed a left adnexal mass consistent with an ovarian teratoma. Management commenced with methylprednisolone boluses and plasma exchanges. This case underlines the importance of ongoing research and collaboration in refining treatment strategies for autoimmune encephalitis patients to improve outcomes and quality of life.
抗N-甲基-D-天冬氨酸受体(NMDAR)脑炎是自身免疫性脑炎最常见的形式,主要影响年轻患者,且女性发病率更高。患者常出现精神症状或认知障碍,如言语紊乱、意识水平下降、自主神经功能障碍,以及由于突触外NMDA受体过度激活导致的癫痫发作、运动障碍和紧张症。迄今为止,紧张症的诊断尚无金标准;然而,有一些评定量表可用于测量这种现象,其中布什-弗朗西斯紧张症评定量表因其有效性、可靠性和易于应用而最为常用。在本病例中,我们报告一名19岁女性,其首发症状包括波动性头痛、心境恶劣、耳鸣和面孔失认症。最终,她出现空间定向障碍和左侧面部感觉减退,以及失眠。随后,她报告有感知觉改变,并伴有大小便失禁。入院时,患者表现为紧张症。腰椎穿刺显示细胞计数、蛋白质和葡萄糖水平正常,血清中存在反应性抗NMDAR抗体,脑电图结果表明存在广泛性功能障碍,符合Graus可能脑炎标准。CT扫描显示左侧附件区有一肿块,与卵巢畸胎瘤相符。治疗开始时给予甲泼尼龙冲击治疗和血浆置换。该病例强调了持续研究和合作对于完善自身免疫性脑炎患者治疗策略以改善预后和生活质量的重要性。