Schaffner Damien, Maitre Guillaume, Lava Sebastiano A G, Boegli Yann, Dolci Mirko, Pfister Raymond, Sekarski Nicole, Marie-Hélène Perez, Di Bernardo Stefano
Pediatric Cardiology Unit, Women Mother and Child Department, Lausanne University Hospital, Switzerland.
Intensive Care Unit, Women Mother and Child Department, Lausanne University Hospital, Switzerland.
Int J Cardiol Congenit Heart Dis. 2022 Aug 10;10:100414. doi: 10.1016/j.ijcchd.2022.100414. eCollection 2022 Dec.
Surgical repair of tetralogy of Fallot is usually performed between 3 and 6 months of age with pulmonary valve-sparing repair promoted for the best long-term result. Through a humanitarian program from developing countries, late complete surgical repair of tetralogy of Fallot has been performed at our institution for many years.
Retrospective analysis of pre- and perioperative data, as well as 30-days outcome of patients older than one year with a confirmed diagnosis of tetralogy of Fallot who had a complete surgical repair between 2005 and 2018 at our institution.
One hundred sixty-five patients were included with a median age of 4.5 years [3.0-6.3], median weight of 13.5 kg [10.9 to 16.5], median transcutaneous oximetry of 78% [70 to 85] and median pulmonary valve annulus Z-score of -1.8 [-3.4 to -0.8]. There was no early surgical mortality. By multivariate analysis, only severe right ventricular hypertrophy, severe right ventricle outflow tract obstruction, and hypoplasia of the main pulmonary artery were independent predictors of failure to preserve the pulmonary annulus at surgical repair.
Late complete surgical repair of tetralogy of Fallot has low mortality and morbidity even when pulmonary valve-sparing repair cannot be successfully performed. The preservation of the pulmonary valve function is significantly associated with shorter ventilation time, ICU and hospital lengths of stay. In the analyzed group of patients, a pulmonary valve-sparing repair cannot be predicted exclusively based on the dimension of the pulmonary valve annulus.
法洛四联症的外科修复通常在3至6个月大时进行,为获得最佳长期效果,提倡保留肺动脉瓣修复术。通过一项针对发展中国家的人道主义项目,我院多年来一直为法洛四联症患者进行晚期完全外科修复。
回顾性分析我院2005年至2018年间确诊为法洛四联症且接受完全外科修复的1岁以上患者的术前和围手术期数据以及30天预后情况。
共纳入165例患者,中位年龄4.5岁[3.0 - 6.3],中位体重13.5千克[10.9至16.5],中位经皮血氧饱和度78%[70至85],中位肺动脉瓣环Z值为 -1.8[-3.4至 -0.8]。无早期手术死亡病例。多因素分析显示,仅重度右心室肥厚、重度右心室流出道梗阻和主肺动脉发育不全是外科修复时无法保留肺动脉环的独立预测因素。
即使无法成功进行保留肺动脉瓣修复术,法洛四联症的晚期完全外科修复术的死亡率和发病率也较低。保留肺动脉瓣功能与缩短通气时间、重症监护病房(ICU)住院时间和住院总时长显著相关。在分析的患者组中,不能仅根据肺动脉瓣环尺寸来预测是否能够进行保留肺动脉瓣修复术。