Rabelo Luis Gisli, Tolman Christine, Jonsdottir Brynja, Gudbjartsson Tomas
Faculty of Medicine, University of Iceland, Reykjavik, Iceland.
Cardiothoracic Department, Landspitali-National University Hospital, Reykjavik, Iceland.
Interdiscip Cardiovasc Thorac Surg. 2024 Dec 25;40(1). doi: 10.1093/icvts/ivae214.
Angiomatoid fibrous histiocytoma (AFH) is a rare soft tissue tumour that rarely behaves malignant. We report a radical resection of a mediastinal angiomatoid fibrous histiocytoma, which grew invasively into the pulmonary artery wall, was adherent to the posterior aorta and close to the main stem of the left coronary artery. A transection of the aorta was performed using cardiopulmonary bypass and cardioplegic arrest for a safe and radical removal that resulted in symptom relief.
血管样纤维组织细胞瘤（AFH）是一种罕见的软组织肿瘤，很少表现为恶性。我们报告了一例纵隔血管样纤维组织细胞瘤的根治性切除术，该肿瘤侵袭性生长至肺动脉壁，与主动脉后壁粘连且靠近左冠状动脉主干。在体外循环和心脏停搏下进行主动脉横断，以实现安全的根治性切除，从而缓解症状。
