Chukwuocha Ikechukwu, Al-Moyeed Baig, Eigbe Solomon, Shukla Shilpi
Department of Neurology, New Cross Hospital, Royal Wolverhampton NHS Trust, Wolverhampton Road, Heath Town, West Midlands, WV10 0QP, United Kingdom.
Oxf Med Case Reports. 2024 Dec 28;2024(12):omae171. doi: 10.1093/omcr/omae171. eCollection 2024 Dec.
The leucine-rich glioma-inactivated protein 1 (LGI1) antibody-related autoimmune encephalitis can occur alone or in the setting of a malignancy and manifest with faciobrachial dystonic seizures (FBDS), cognitive decline, hyponatremia, and neuropsychiatric disorders. The importance of differentiating this entity from acute delirium cannot be overemphasized. This review provides a detailed account of a 71-year-old man with previous diagnosis of lung cancer who presented with subacute onset behavioural changes, urinary retention, and FBDS. Investigation revealed hyponatremia, bilateral mesial temporal lobe high signal abnormality worse on the right on MRI and CSF positive anti-LGI1 antibodies (1:30). The patient was treated with immunosuppressive therapy with consequent symptom improvement. This case emphasizes the need to have a high index of suspicion for this disease entity in patients presenting with new onset behavioural changes and the importance of identifying the typical FBDS, as early initiation of treatment confers a positive outcome for diseased patients.
富含亮氨酸的胶质瘤失活蛋白1(LGI1)抗体相关的自身免疫性脑炎可单独发生或在恶性肿瘤背景下出现,表现为面臂肌张力障碍性癫痫发作(FBDS)、认知功能下降、低钠血症和神经精神障碍。将这种疾病与急性谵妄区分开来的重要性再怎么强调也不为过。本综述详细介绍了一名71岁男性,既往诊断为肺癌,出现亚急性起病的行为改变、尿潴留和FBDS。检查发现低钠血症,MRI显示双侧内侧颞叶高信号异常,右侧更明显,脑脊液抗LGI1抗体阳性(1:30)。患者接受免疫抑制治疗后症状改善。该病例强调,对于出现新发行为改变的患者,需要高度怀疑这种疾病,识别典型的FBDS很重要,因为早期开始治疗会给患病患者带来积极的结果。