Zhu Yibei, McCloskey Olivia, Robinson Justin A, Stewart Robert D, Patel Chandrakant R, Breedlove Kristen, Karamlou Tara
Case Western Reserve University School of Medicine, Cleveland, OH, USA.
Department of Thoracic and Cardiovascular Surgery, Cleveland Clinic, Cleveland, OH, USA.
J Cardiothorac Surg. 2025 Jan 5;20(1):19. doi: 10.1186/s13019-024-03320-7.
Pulmonary artery sling (PAS) is a rare congenital anomaly where the left pulmonary artery (LPA) branches from the right pulmonary artery, compressing the trachea and esophagus and frequently leading to respiratory distress in infants. Surgical intervention, such as LPA reimplantation or translocation, is crucial to relieve airway compression and restore normal pulmonary function.
This report highlights varied LPA anatomies, including a unique case of an anomalous LPA without true sling formation but causing tracheal compression, alongside two typical PAS cases. Respiratory symptoms were successfully mitigated in all three cases without concomitant tracheal reconstruction.
This report underscores the necessity of thorough preoperative assessment of airway anatomy and highlight the importance of individualized surgical planning for anomalous LPA.
肺动脉吊带(PAS)是一种罕见的先天性异常,其中左肺动脉(LPA)起源于右肺动脉,压迫气管和食管,并常常导致婴儿呼吸窘迫。手术干预,如LPA重新植入或移位,对于缓解气道压迫和恢复正常肺功能至关重要。
本报告重点介绍了不同的LPA解剖结构,包括一例独特的无真正吊带形成但导致气管压迫的异常LPA病例,以及两例典型的PAS病例。所有三例患者的呼吸道症状均成功缓解,且未同时进行气管重建。
本报告强调了术前对气道解剖进行全面评估的必要性,并突出了针对异常LPA进行个体化手术规划的重要性。