Nguyen Quynh, Bourke Rachel, Gilbert Richard W, Oldani Graziano, Kim Jong Moo, Lytle Andrew, Cook Richard C, Grocott Hilary P, Price Joel
Division of Cardiac Surgery, University of British Columbia, Vancouver, British Columbia, Canada.
Department of Anesthesiology, Pharmacology & Therapeutics, University of British Columbia, Vancouver, British Columbia, Canada.
Ann Thorac Surg Short Rep. 2024 Mar 29;2(3):544-547. doi: 10.1016/j.atssr.2024.03.003. eCollection 2024 Sep.
Rosai-Dorfman disease (RDD) is a nonmalignant disease of histiocyte proliferation. RDD usually presents with painless cervical lymphadenopathy, although extranodal involvement can occur. Cardiac involvement was reported in <0.1% of cases. We present a case of cardiac RDD with obstruction at the inferior vena cava-right atrial junction.
罗萨伊-多夫曼病(RDD)是一种组织细胞增殖性非恶性疾病。RDD通常表现为无痛性颈部淋巴结病,不过也可能出现结外受累情况。据报道,心脏受累的病例不到0.1%。我们报告一例发生于下腔静脉-右心房交界处并伴有梗阻的心脏RDD病例。