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重新定义阴道发育不全的管理:全面综述

Redefining Vaginal Agenesis Management: A Comprehensive Review.

作者信息

Saravanakumar Prathibha, Selvam Divyabharathi, K S Anusha, Maheswari Uma, Jeyapalan Karthigeyan

机构信息

Prosthodontics, Sri Ramachandra Institute of Higher Education and Research, Chennai, IND.

Prosthodontics, SRM Dental College, Chennai, IND.

出版信息

Cureus. 2024 Dec 25;16(12):e76366. doi: 10.7759/cureus.76366. eCollection 2024 Dec.

DOI:10.7759/cureus.76366
PMID:39867053
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11759661/
Abstract

Vaginal agenesis, a rare and complex congenital anomaly predominantly linked to Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome or complete androgen insensitivity syndrome (CAIS), demands innovative and highly individualized treatment strategies to achieve anatomical and functional restoration. While non-surgical options like vaginal dilation remain foundational, the advent of custom-made stents has redefined the paradigm of care, emerging as a transformative tool in both post-surgical and non-surgical management. Bridging the expertise of prosthodontics and gynecology, personalized stents not only enhance healing and maintain patency but also elevate patient comfort and compliance. Prosthodontists, leveraging advanced material science and precision design, play a critical role in crafting bespoke stents tailored to anatomical and therapeutic needs. This review highlights the synergistic relationship between prosthodontics and gynecology, emphasizing the cutting-edge role of custom stents in improving outcomes for patients with vaginal agenesis.

摘要

阴道发育不全是一种罕见且复杂的先天性异常,主要与迈耶-罗基坦斯基-库斯特-豪泽综合征(MRKH综合征)或完全性雄激素不敏感综合征(CAIS)相关,需要创新且高度个性化的治疗策略来实现解剖结构和功能的恢复。虽然诸如阴道扩张等非手术选择仍然是基础,但定制支架的出现重新定义了护理模式,成为手术和非手术治疗中的变革性工具。融合了口腔修复学和妇科专业知识的个性化支架不仅能促进愈合、保持通畅,还能提升患者的舒适度和依从性。口腔修复医生利用先进的材料科学和精确设计,在制作符合解剖和治疗需求的定制支架方面发挥着关键作用。本综述强调了口腔修复学与妇科之间的协同关系,着重阐述了定制支架在改善阴道发育不全患者治疗效果方面的前沿作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bd9c/11759661/5d5f9f618d85/cureus-0016-00000076366-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bd9c/11759661/5d5f9f618d85/cureus-0016-00000076366-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bd9c/11759661/5d5f9f618d85/cureus-0016-00000076366-i01.jpg

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本文引用的文献

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Comprehensive management of Mayer-Rokitansky-Küster-Hauser syndrome management: A case report.Mayer-Rokitansky-Küster-Hauser综合征的综合管理:一例报告
Narra J. 2024 Aug;4(2):e755. doi: 10.52225/narra.v4i2.755. Epub 2024 Jul 9.
2
Fabrication of Hollow Acrylic Vaginal Stents Using Frozen Coconut Oil for Vaginal Agenesis Management.使用冷冻椰子油制造中空丙烯酸阴道支架用于阴道发育不全的治疗
Cureus. 2024 May 17;16(5):e60512. doi: 10.7759/cureus.60512. eCollection 2024 May.
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Design and Material Characterization of an Inflatable Vaginal Dilator.
一种可充气阴道扩张器的设计与材料特性
Materials (Basel). 2024 Feb 24;17(5):1050. doi: 10.3390/ma17051050.
4
Customised Vaginal Stent-The Phases in Management of Vaginal Agenesis in Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome.定制阴道支架——迈耶-罗基坦斯基-库斯特-豪泽综合征(MRKH综合征)阴道发育不全管理的各个阶段
J Family Reprod Health. 2023 Mar;17(1):54-57. doi: 10.18502/jfrh.v17i1.11978.
5
Three-dimensional Printer Molds for Vaginal Agenesis: An Individualized Approach as Conservative Treatment.三维打印机模具治疗阴道闭锁:个体化方法作为保守治疗。
Rev Bras Ginecol Obstet. 2022 Dec;44(12):1110-1116. doi: 10.1055/s-0042-1756214. Epub 2022 Sep 22.
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Treatment for vaginal agenesis: A prospective and comparative study between vaginal dilation and surgical neovaginoplasty.阴道发育不全的治疗:阴道扩张术与手术新阴道成形术的前瞻性对比研究。
Int J Gynaecol Obstet. 2022 Jun;157(3):574-581. doi: 10.1002/ijgo.13931. Epub 2021 Oct 4.
7
Hollow vaginal stent for a case of Mayer-Rokitansky-Kuster-Hauser syndrome: a case report.用于 Mayer-Rokitansky-Kuster-Hauser 综合征一例的中空阴道支架:病例报告。
Pan Afr Med J. 2021 Apr 9;38:343. doi: 10.11604/pamj.2021.38.343.28837. eCollection 2021.
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Laparoscopic Davydov's Colpopoiesis for a Case of Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome.腹腔镜下Davydov阴道成形术治疗1例苗勒管发育不全综合征(MRKH综合征)
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Fertil Steril. 2021 Mar;115(3):804-806. doi: 10.1016/j.fertnstert.2020.09.030. Epub 2020 Dec 4.
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Orphanet J Rare Dis. 2020 Aug 20;15(1):214. doi: 10.1186/s13023-020-01491-9.