Jeon Hyun Min, Noh Hae Sook, Jeon Min-Gyu, Park Jin-Ho, Lee Young-Sun, Seo Gyunghwa, Cheon Yun-Hong, Kim Mingyo, Han Myung-Kwan, Park Jae-Yong, Lee Sang-Il
Division of Rheumatology, Department of Internal Medicine and Institute of Medical Science, Gyeongsang National University School of Medicine and Gyeongsang National University Hospital, Jinju, South Korea.
School of Biosystem and Biomedical Science, College of Health Science, Korea University, Seoul, South Korea.
Exp Mol Med. 2025 Feb;57(2):335-348. doi: 10.1038/s12276-025-01393-5. Epub 2025 Feb 3.
Fibroblast-like synoviocytes (FLSs), which are stromal cells that play key roles in rheumatoid arthritis (RA) pathophysiology, are characterized by a tumor-like phenotype and immunostimulatory actions. C2 domains in various proteins play roles in intracellular signaling and altering cellular characteristics, and some C2 domain-containing proteins exacerbate or alleviate certain malignant or inflammatory diseases. However, the roles of C2 domains in regulating the functions of RA FLSs remain unclear. Here we performed functional C2 domainomics with 144 C2 domain-containing viral vectors and identified the C2 domain of PLCη2 as a key regulator of RA FLSs. In mice, overexpressing PLCη2 or only its C2 domain PLCη2 (PLCη2_C2) diminished the proliferation, migration, invasion and inflammatory responses of RA FLSs, mitigating RA pathology; the absence of PLCη2 amplified these proinflammatory and destructive processes in RA FLSs in vivo. Mechanistically, PLCη2 and PLCη2_C2 participate in the pathological signaling of RA FLSs in a calcium-independent manner through protein-protein interactions. Specifically, PLCη2_C2 disrupted HRAS-RAF1 interactions, suppressing downstream signaling pathways, including the NF-κB, JAK-STAT and MAPK pathways. Collectively, these findings establish PLCη2 and PLCη2_C2 as novel inhibitory regulators in RA, suggesting promising therapeutic avenues for addressing FLS-driven disease mechanisms.
成纤维样滑膜细胞(FLSs)是在类风湿性关节炎(RA)病理生理学中起关键作用的基质细胞,其特征在于肿瘤样表型和免疫刺激作用。各种蛋白质中的C2结构域在细胞内信号传导和改变细胞特性中发挥作用,并且一些含C2结构域的蛋白质会加重或减轻某些恶性或炎性疾病。然而,C2结构域在调节RA FLSs功能中的作用仍不清楚。在这里,我们用144种含C2结构域的病毒载体进行了功能性C2结构域组学研究,并确定PLCη2的C2结构域是RA FLSs的关键调节因子。在小鼠中,过表达PLCη2或仅其C2结构域PLCη2_C2可减少RA FLSs的增殖、迁移、侵袭和炎症反应,减轻RA病理;缺乏PLCη2会在体内放大RA FLSs中的这些促炎和破坏过程。从机制上讲,PLCη2和PLCη2_C2通过蛋白质-蛋白质相互作用以钙非依赖性方式参与RA FLSs的病理信号传导。具体而言,PLCη2_C2破坏了HRAS-RAF1相互作用,抑制了包括NF-κB、JAK-STAT和MAPK途径在内的下游信号通路。总之,这些发现确立了PLCη2和PLCη2_C2作为RA中的新型抑制调节因子,为解决FLS驱动的疾病机制提供了有前景的治疗途径。