Farvardin Hajar, Farvardin Majid, Zare Kamran
Poostchi Ophthalmology Research Center, Department of Ophthalmology, School of Medicine, Shiraz University of Medical Sciences, Shiraz, Iran.
Rom J Ophthalmol. 2024 Oct-Dec;68(4):439-442. doi: 10.22336/rjo.2024.79.
Duane Retraction Syndrome (DRS) and Monocular Elevation Deficiency (MED) are two distinct congenital strabismus entities that have not been reported simultaneously until now. Thirty percent of individuals with DRS present with various congenital ocular and non-ocular anomalies. A 16-year-old girl presented with right eye ptosis and ocular deviation since birth. The patient's hypotropia increased in the upward gaze. She also exhibited small-angle exotropia in the primary position, along with the limitation of both abduction and adduction. The patient had globe retraction and increased ptosis in adduction. Strabismus manifestation in the patient was consistent with concurrent type III DRS and MED in the right eye.
杜安眼球后退综合征(DRS)和单眼上睑下垂(MED)是两种不同的先天性斜视类型,此前尚未有同时报道的情况。30%的DRS患者伴有各种先天性眼部和非眼部异常。一名16岁女孩自出生起就出现右眼上睑下垂和眼球偏斜。患者向上注视时下斜视加重。她在第一眼位还表现出小角度外斜视,同时伴有外展和内收受限。患者内收时眼球后退且上睑下垂加重。该患者的斜视表现符合右眼同时存在III型DRS和MED。