Goodarzi Amir, Toussi Atrin, Lechpammer Mirna, Lee Darrin, Shahlaie Kiarash
Department of Neurological Surgery, University of California, Davis, California, USA.
Department of Pathology, University of California, Davis, California, USA.
World Neurosurg. 2017 Nov;107:1052.e11-1052.e16. doi: 10.1016/j.wneu.2017.08.124. Epub 2017 Sep 1.
Chordomas are rare, notochord-derived neoplasms. Of these tumors, intradural chordomas are exceedingly rare. Most occur within the prepontine, parasellar, or other midline intradural locations. An intradural chordoma arising from the cerebellopontine angle has not been described previously.
We describe the first case of an intradural chordoma originating from the left cerebellopontine angle resected over the course of 2 operations.
Intradural chordomas are rare and can arise anywhere in the posterior fossa. Lack of bony involvement on computed tomography and magnetic resonance imaging are indicative of this pathology when there is also a lack of markers indicating the presence of more common cerebellopontine angle tumors. Treatment goals should include gross total resection and possible radiation therapy.
脊索瘤是一种罕见的、源自脊索的肿瘤。在这些肿瘤中，硬膜内脊索瘤极其罕见。大多数发生在脑桥前、鞍旁或其他中线硬膜内位置。此前尚未有源自小脑脑桥角的硬膜内脊索瘤的相关描述。
我们描述了首例经两次手术切除的源自左侧小脑脑桥角的硬膜内脊索瘤病例。
硬膜内脊索瘤罕见，可发生于后颅窝的任何部位。当计算机断层扫描和磁共振成像显示无骨质受累且缺乏提示更常见的小脑脑桥角肿瘤存在的标志物时，可提示这种病理情况。治疗目标应包括全切除以及可能的放射治疗。
