偶然发现的伴有完全性内脏反位、下腔静脉中断和支气管扩张的成人多脾综合征

Arora Kanupriya, Verma Mansi, Makhaik Sushma

Indira Gandhi Medical College, Shimla, India.

Methodist Debakey Cardiovasc J. 2025 Mar 6;21(1):6-9. doi: 10.14797/mdcvj.1537. eCollection 2025.

Incidental detection of polysplenia associated with situs inversus totalis in an adult is rarely reported in literature.12 "Heterotaxy" refers to a wide spectrum of anomalies involving dysmorphism of thoracoabdominal organs across the right-left axis of the body. Polysplenia is observed in left isomerism along with bilateral bilobed bronchi and bilateral morphologic left atria. However, in this case, polysplenia was present without isomerism.

成人中偶然发现多脾症合并完全性内脏反位的情况在文献中鲜有报道。“内脏异位”指的是一系列涉及胸腹部器官在身体左右轴线上形态异常的病症。多脾症在左位异构中可见，同时伴有双侧双叶支气管和双侧形态学上的左心房。然而，在本病例中，多脾症存在但无异构现象。