Macular Morphological Changes in Familial Exudative Vitreoretinopathy with Macular Traction on OCT.

INTRODUCTION

We aimed to report macular morphological changes observed on optical coherence tomography (OCT) in a child with familial exudative vitreoretinopathy (FEVR), experiencing macular traction caused by fibrovascular tissue (FT), who underwent vitrectomy.

CASE PRESENTATION

A 7-year-old girl presented with the chief complaint of decreased visual acuity in the left eye during a school examination. Fundus examination revealed retinal folds with FT extending from the peripheral retina to the posterior pole of the left eye. Despite interventions such as retinal photocoagulation and encircling buckling aimed at reducing the traction on the macula, OCT revealed persistent deep retinal folds and a thickened outer nuclear layer (ONL), indicating gradually increasing macular traction, which contributed to vision loss. A subsequent vitrectomy alleviated the macular traction, enhanced the retinal morphology, and reduced ONL thickening regardless of persistent ectopic inner foveal layers.

CONCLUSIONS

Macular morphological changes before and after vitrectomy in a pediatric case of FEVR can be observed using OCT. Vitrectomy with FT removal may be effective in partially improving macular morphology in FEVR with macular traction.