一名成年运动员被诊断出左肺动脉起源于降主动脉异常。
Anomalous Origin of Left Pulmonary Artery From the Descending Aorta Diagnosed in an Athletic Adult.
作者信息
Touray Mariama, Fahrni Guillaume, Rutz Tobias, Bouchardy Judith, Yerly Patrick, Touray Aisha, Ladouceur Magalie
机构信息
Cardiothoracic and Vascular Division, Lausanne University Hospital, Lausanne, Switzerland.
Department of Diagnostic and Interventional Radiology, University Hospital of Lausanne, Switzerland.
出版信息
JACC Case Rep. 2025 Apr 2;30(7):103407. doi: 10.1016/j.jaccas.2025.103407.
BACKGROUND
Anomalous origin of the left pulmonary artery from the aorta, also named hemitruncus arteriosus, is a rare congenital heart disease associated with high mortality. Patients are usually operated on in the first months of life to avoid irreversible damage caused by pulmonary arterial hypertension.
CASE SUMMARY
The authors present a challenging case of an athletic male patient with an anomalous left pulmonary artery originating from the descending aorta that was diagnosed when he was aged 27 years, with severe segmental pulmonary arterial hypertension in the left lung. Following multidisciplinary team meetings, conservative management was chosen.
DISCUSSION
Multimodality imaging plays a key role in both diagnosing and managing this birth defect and its potential complications.
TAKE-HOME MESSAGE: Management of this extremely rare congenital anomaly in the adult is yet to be fully understood and requires a multidisciplinary team in a tertiary center.
背景
左肺动脉起源于主动脉异常，也称为半动脉干，是一种罕见的先天性心脏病，死亡率很高。患者通常在出生后的头几个月接受手术，以避免肺动脉高压造成的不可逆转的损害。
病例摘要
作者介绍了一例具有挑战性的病例，一名运动型男性患者，其左肺动脉起源于降主动脉异常，在27岁时被诊断出，左肺有严重的节段性肺动脉高压。经过多学科团队会诊后，选择了保守治疗。
讨论
多模态成像在诊断和管理这种先天性缺陷及其潜在并发症方面起着关键作用。
要点
成人这种极其罕见的先天性异常的管理尚未完全明确，需要三级中心的多学科团队进行处理。
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