Sachani Pratiksha, Dhande Rajasbala, Parihar Pratapsingh, Kasat Paschyanti, Pradeep Utkarsh
Department of Radiology, Jawaharlal Nehru Medical College, Datta Meghe Institute of Higher Education & Research, Wardha, India.
Department of Medicine, Jawaharlal Nehru Medical College, Datta Meghe Institute of Higher Education & Research, Wardha, India.
Radiol Case Rep. 2025 Mar 20;20(6):2855-2860. doi: 10.1016/j.radcr.2025.02.089. eCollection 2025 Jun.
Hemophilia is a genetic disorder that manifests due to a deficiency of clotting factors. One of the most common complications is hemophilic arthropathy which results in bleeding into large joints causing hemosiderin deposition. Recurrent hemarthrosis causes joint destruction resulting in pain and a decreased range of movements. Radiological imaging is essential for staging, prognostication, and treatment protocol. X-rays show the extent of joint destruction and narrowing of joint space. Ultrasonography helps in visualizing tendons and joint effusion. However magnetic resonance imaging is the gold standard for staging hemophilic arthropathy. Management involves both medical and surgical intervention as per the level of joint involvement.
血友病是一种由于凝血因子缺乏而表现出的遗传性疾病。最常见的并发症之一是血友病性关节病，它会导致大关节出血，引起含铁血黄素沉积。反复的关节积血会导致关节破坏，从而引起疼痛和活动范围减小。放射影像学对于分期、预后评估和治疗方案至关重要。X线显示关节破坏程度和关节间隙变窄。超声有助于观察肌腱和关节积液。然而，磁共振成像才是血友病性关节病分期的金标准。治疗根据关节受累程度涉及医学和外科干预。
