Suppr超能文献

一例儿童先天性黑素细胞痣的成功分期切除手术:病例报告

A successful serial excision surgery for congenital melanocytic nevus in a child: A case report.

作者信息

Al Sakka Amini Ruaa, Hakmi Abdulhafiz, Hendi Hamza, Abo Saada Sawsan, Etr Aladdin

机构信息

Abdali hospital, Amman, Jordan.

Ain Shams University, Cairo, Egypt.

出版信息

Int J Surg Case Rep. 2025 May;130:111297. doi: 10.1016/j.ijscr.2025.111297. Epub 2025 Apr 18.

Abstract

INTRODUCTION AND IMPORTANCE

Giant congenital melanocytic nevi (GCMN) are rare, large pigmented lesions present at birth that can significantly impact a patient's physical appearance and psychological well-being.

CASE PRESENTATION

This case report presents a successful outcome of serial surgical excision for a GCMN in a 10-year-old Syrian male. The patient presented with a large GCMN covering his entire nose and part of his left infraorbital region, causing significant psychological distress. Despite no immediate symptoms, a staged approach using serial surgical excisions and skin grafting was applied, resulting in the complete removal of the GCMN over 18 months. The patient experienced no significant complications and achieved a successful aesthetic result, allowing him to return to school and resume normal activities.

CLINICAL DISCUSSION

The best treatment for congenital melanocytic nevi (CMN) is uncertain and varies based on the nevus characteristics. However, early excision of large nevi can reduce melanoma risk and relieve psychological distress for both the child and parents.

CONCLUSION

Congenital melanocytic nevi (CMN) are rare benign lesions that can potentially become malignant, affecting patients' well-being. This case highlights the effectiveness of serial surgical excision in managing GCMN, demonstrating the potential for successful outcomes even in complex cases.

摘要

引言与重要性

巨大先天性黑素细胞痣(GCMN)是出生时就存在的罕见、巨大色素沉着病变,会对患者的外貌和心理健康产生重大影响。

病例介绍

本病例报告展示了一名10岁叙利亚男性患者的巨大先天性黑素细胞痣经系列手术切除取得成功的结果。该患者出现一个巨大先天性黑素细胞痣,覆盖其整个鼻子和部分左眶下区域,造成严重的心理困扰。尽管当时没有直接症状,但采用了系列手术切除和皮肤移植的分期方法,在18个月内成功完全切除了巨大先天性黑素细胞痣。患者未出现重大并发症,取得了成功的美学效果,使其能够重返学校并恢复正常活动。

临床讨论

先天性黑素细胞痣(CMN)的最佳治疗方法尚不确定,且因痣的特征而异。然而,早期切除大的痣可降低黑色素瘤风险,并减轻患儿及其父母的心理困扰。

结论

先天性黑素细胞痣(CMN)是罕见的良性病变,有可能恶变,影响患者的健康。本病例突出了系列手术切除在处理巨大先天性黑素细胞痣方面的有效性,表明即使在复杂病例中也有取得成功结果的潜力。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3cc6/12033938/271b5316794f/gr1.jpg

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验