Akça Fatma, Yazıcıoğlu Levent, Hasde Ali İhsan, Büyükçakır Onur, Özdemir Deniz Ladin
Department of Cardiovascular Surgery, Kırıkkale High Specialization Hospital, Kırıkkale, Türkiye.
Department of Cardiovascular Surgery, Ankara University Faculty of Medicine, Ankara, Türkiye.
Turk Gogus Kalp Damar Cerrahisi Derg. 2024 Dec 31;32(4 Suppl 2):133-134. doi: 10.5606/tgkdc.dergisi.2024.mep-35. eCollection 2024 Nov.
Cardiac tumors mainly present as metastases from tumors in other extracardiac organs. Primary cardiac tumors are relatively rare tumors, with a prevalence rate of 0.002 to 0.33%. Myxomas, which commonly occur in the left atrium, are the most frequent benign primary cardiac tumors. Angiosarcomas are the most common primary malignant cardiac tumors. A 63-year-old female patient who had exertional dyspnea presented to the clinic. After the detection of an invasive mass on the wall of the right atrium from the test results, the case was initiated following sternotomy, with aortic and peripheral venous cannulation. The right atrium was opened, and the tumor was dissected broadly from the normal tissue of the atrium wall. The right atrial defect was reconstructed with a pericardial patch. After extensive tumor resection and repair with a pericardial patch, the patient was transferred to the intensive care unit with inotropic support. The pathology result of the excised material was reported as angiosarcoma. The patient was discharged on the seventh postoperative day and continued with chemoradiotherapy. Cardiac tumors are rare, and angiosarcomas, which are more commonly observed on the right side of the heart, account for 25 to 30% of primary cardiac malignancies. Surgical resection of primary cardiac angiosarcoma is the primary treatment approach. Full resection of the tumor offers long-term survival for the patients. Reconstruction of cardiac structures may also be necessary after wide resections.
心脏肿瘤主要表现为其他心外器官肿瘤的转移。原发性心脏肿瘤是相对罕见的肿瘤,患病率为0.002%至0.33%。黏液瘤通常发生于左心房,是最常见的原发性良性心脏肿瘤。血管肉瘤是最常见的原发性恶性心脏肿瘤。一名63岁有劳力性呼吸困难的女性患者到诊所就诊。检查结果发现右心房壁有一浸润性肿块后,该病例在开胸术后开始,进行主动脉和外周静脉插管。打开右心房,将肿瘤从心房壁正常组织广泛剥离。用心包补片修复右心房缺损。在广泛切除肿瘤并用心包补片修复后,患者在给予正性肌力支持的情况下被转入重症监护病房。切除组织的病理结果报告为血管肉瘤。患者术后第7天出院,并继续进行放化疗。心脏肿瘤罕见,血管肉瘤更常见于心脏右侧,占原发性心脏恶性肿瘤的25%至30%。原发性心脏血管肉瘤的手术切除是主要治疗方法。肿瘤的完整切除为患者提供长期生存。广泛切除后也可能需要重建心脏结构。