一名因胶原蛋白VI相关型肌营养不良导致身材极度矮小和体重过低的女性怀孕。
Pregnancy in a woman with extreme short stature and low body weight secondary to a collagen VI-related muscular dystrophy.
作者信息
O'Sullivan Joseph, Mahmood Hifsa, Curry Ruth A, Frise Charlotte
机构信息
Oxford University Hospitals NHS Foundation Trust, Oxford, UK.
Imperial College Healthcare NHS Trust, London, UK.
出版信息
Obstet Med. 2025 Jun;18(2):123-126. doi: 10.1177/1753495X231219298. Epub 2023 Dec 21.
Abstract
Pregnancy poses significant physiological demands, and women of extreme short stature may be particularly at risk of complications. Described here are two pregnancies in a woman who was 130 cm tall with a body mass index of 12 kg/m and the maternal and neonatal outcomes. The challenges encountered in the care of our patient included cardiorespiratory compromise, management of medication dosing, management of delivery and bleeding risk.
摘要
怀孕对生理有重大需求，身材极矮的女性可能尤其容易出现并发症。本文描述了一名身高130厘米、体重指数为12kg/m²的女性的两次怀孕情况以及母婴结局。在护理我们的患者过程中遇到的挑战包括心肺功能不全、药物剂量管理、分娩管理和出血风险。
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