Nonnemacher Cory, Saylors Seth, Denning Naomi-Liza, Melkonian Vatche, Aguayo Pablo
Pediatric Surgery, Children's Mercy Hospital, Kansas City, USA.
Cureus. 2025 Apr 11;17(4):e82082. doi: 10.7759/cureus.82082. eCollection 2025 Apr.
Intestinal atresias are a common cause of neonatal intestinal obstruction. An extremely rare variant is total intestinal atresia, where no lumen is appreciable from the duodenum through the colon. We describe a case of a 33-week female who was born at an outside hospital and underwent laparotomy for concern for intrauterine perforation and proximal intestinal obstruction. Laparotomy revealed a duodenal perforation and an atresia in the proximal jejunum. Resection of this segment revealed no intestinal lumen distally, and the patient was left in discontinuity and transferred to our tertiary children's hospital. Repeat laparotomy revealed atretic bowel with no lumen through the colon with a normal appearing mesentery. A decompressive gastrostomy tube was placed, and the patient passed away after withdrawal of care. Total intestinal atresia is a rare variation of intestinal atresia with no current surgical or medical treatments.
肠道闭锁是新生儿肠梗阻的常见原因。一种极其罕见的类型是全肠道闭锁，即从十二指肠到结肠均无明显管腔。我们描述了一例33周龄的女婴，她在外院出生，因担心子宫内穿孔和近端肠梗阻而接受了剖腹手术。剖腹手术发现十二指肠穿孔和近端空肠闭锁。切除该段肠管后发现远端无肠腔，患者肠管连续性中断，随后被转至我们的三级儿童医院。再次剖腹手术发现结肠全程肠管闭锁且无管腔，但肠系膜外观正常。放置了减压胃造瘘管，患者在停止治疗后死亡。全肠道闭锁是肠道闭锁的一种罕见类型，目前尚无手术或药物治疗方法。
