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一例罕见的因腱索条索帐篷样改变继发严重主动脉瓣反流病例:一种用于具有挑战性诊断的多模态成像方法

A Rare Case of Severe Aortic Regurgitation Secondary to Tenting of Chordae Tendineae Strands: A Multimodality Imaging Approach for a Challenging Diagnosis.

作者信息

Catapano Dario, Dellegrottaglie Santo, Scatteia Alessandra, Gallinoro Carlo Maria, Pascale Carmine Emanuele, Falco Luigi, Di Lorenzo Emilio, Masarone Daniele

机构信息

Department of Translational Medical Sciences, University of Campania "Luigi Vanvitelli", Via Leonardo Bianchi 1, 80131 Naples, Italy.

Advanced Cardiovascular Imaging Unit, Clinica Villa dei Fiori, 80011 Acerra, Italy.

出版信息

Diagnostics (Basel). 2025 Apr 23;15(9):1071. doi: 10.3390/diagnostics15091071.

DOI:10.3390/diagnostics15091071
PMID:40361888
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12071409/
Abstract

We discuss a case of a patient who was referred to our department for an in-depth evaluation of aortic regurgitation severity and its underlying causes. By employing a multimodal imaging strategy that combined transthoracic echocardiography (TTE), transesophageal echocardiography (TEE), and cardiac magnetic resonance imaging (cMRI), we successfully identified a particularly rare cause of aortic regurgitation: chordae tendineae that lead to asymmetric retraction of the aortic cusps. Furthermore, this approach provided a clearer understanding of the aortic root anatomy and the hemodynamic effects of the regurgitant flow on the ventricle. This case demonstrates the diagnostic effectiveness of various imaging techniques and emphasizes the crucial importance of multimodal imaging for a thorough assessment of aortic valvular issues.

摘要

我们讨论了一例患者,该患者被转诊至我科,以深入评估主动脉瓣反流的严重程度及其潜在病因。通过采用一种多模态成像策略,该策略结合了经胸超声心动图(TTE)、经食管超声心动图(TEE)和心脏磁共振成像(cMRI),我们成功地确定了一种特别罕见的主动脉瓣反流病因:导致主动脉瓣叶不对称回缩的腱索。此外,这种方法能更清晰地了解主动脉根部解剖结构以及反流血流对心室的血流动力学影响。该病例展示了各种成像技术的诊断效果,并强调了多模态成像对于全面评估主动脉瓣问题的至关重要性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3278/12071409/cd63856331b4/diagnostics-15-01071-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3278/12071409/08b6ccbf7797/diagnostics-15-01071-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3278/12071409/b5ad67521213/diagnostics-15-01071-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3278/12071409/cd63856331b4/diagnostics-15-01071-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3278/12071409/08b6ccbf7797/diagnostics-15-01071-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3278/12071409/b5ad67521213/diagnostics-15-01071-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3278/12071409/cd63856331b4/diagnostics-15-01071-g003.jpg

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本文引用的文献

1
The extremely rare case of aortic chordae tendineae strands: A case report with literature review.主动脉腱索罕见病例:病例报告并文献复习
Clin Case Rep. 2023 Oct 10;11(10):e8033. doi: 10.1002/ccr3.8033. eCollection 2023 Oct.
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