Ramadan Mahmoud M, Al-Najjar Raghad A, Abady Rokia S, Obaid Hala A, Mostafa Yasmeen A, Al-Obeid Mohammad T, Elmahal Mohammed
Cardiology, Faculty of Medicine, Mansoura University, Mansoura, EGY.
Clinical Sciences, College of Medicine, University of Sharjah, Sharjah, ARE.
Cureus. 2025 Apr 21;17(4):e82722. doi: 10.7759/cureus.82722. eCollection 2025 Apr.
Mavacamten is a first-in-class, selective allosteric inhibitor of cardiac myosin adenosine triphosphatase (ATPase) that has emerged as a novel therapeutic option for patients with symptomatic hypertrophic obstructive cardiomyopathy (HOCM) who remain refractory to conventional therapy, such as beta-blockers and calcium channel blockers. Clinical trials have demonstrated that mavacamten reduces left ventricular outflow tract (LVOT) obstruction, improves diastolic function, and enhances exercise capacity, thereby addressing the key pathophysiological mechanisms underlying HOCM. However, its use requires careful dose titration due to the potential for reversible reductions in left ventricular ejection fraction (LVEF). While mavacamten represents a meaningful therapeutic advancement in HOCM management, its role in other conditions such as non-obstructive hypertrophic cardiomyopathy (HCM) and heart failure with preserved ejection fraction (HFpEF) remains investigational. Preliminary data suggest favorable effects on diastolic parameters and cardiac biomarkers in HFpEF, but larger studies are needed to establish efficacy. While these challenges persist, ongoing research is exploring broader cardiomyopathy populations, optimization of combination therapies, and development of novel formulations. As a targeted modulator of myocardial contractility, mavacamten exemplifies the shift toward mechanism-based, precision therapeutics in cardiovascular medicine.
玛伐卡坦是一种一流的、选择性变构心肌肌球蛋白三磷酸腺苷酶(ATP酶)抑制剂,已成为对传统疗法(如β受体阻滞剂和钙通道阻滞剂)仍难治的有症状肥厚性梗阻性心肌病(HOCM)患者的一种新型治疗选择。临床试验表明,玛伐卡坦可减轻左心室流出道(LVOT)梗阻,改善舒张功能,并增强运动能力,从而解决HOCM潜在的关键病理生理机制。然而,由于其可能导致左心室射血分数(LVEF)可逆性降低,使用时需要仔细调整剂量。虽然玛伐卡坦在HOCM治疗方面代表了一项有意义的治疗进展,但其在其他疾病如非梗阻性肥厚型心肌病(HCM)和射血分数保留的心力衰竭(HFpEF)中的作用仍在研究中。初步数据表明对HFpEF的舒张参数和心脏生物标志物有有利影响,但需要更大规模的研究来确定其疗效。尽管这些挑战仍然存在,但正在进行的研究正在探索更广泛的心肌病群体、优化联合治疗以及开发新型制剂。作为心肌收缩力的靶向调节剂,玛伐卡坦体现了心血管医学向基于机制的精准治疗的转变。