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一例高钾血症诱发的Brugada波伪像:一种罕见但严重的心电图假象。

A case of Hyperkalemia-induced Brugada Phenocopy: a rare but serious electrocardiographic imposter.

作者信息

Rezkalla Abraam, Rajab Islam, Milhem Fathi, Hattab Moath, Shamoon Yezin, Shamoon Fayez

机构信息

St. Joseph's University Medical Center, Department of Internal Medicine, Paterson, NJ 07470, United States.

Department of Medicine, An Najah National University, Nablus, Palestine.

出版信息

Oxf Med Case Reports. 2025 May 28;2025(5):omaf036. doi: 10.1093/omcr/omaf036. eCollection 2025 May.

DOI:10.1093/omcr/omaf036
PMID:40443850
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12118059/
Abstract

Brugada Syndrome is a potentially fatal, hereditary cardiac disorder that may precipitate sudden cardiac death if not identified. An electrocardiogram (ECG) revealing a characteristic coved ST segment elevation followed by negative T wave in a right-sided precordial lead is pathognomonic for the Brugada pattern. Recently it has been shown that certain abnormalities, such as an electrolyte disturbance, may precipitate a Brugada pattern on ECG. Once the precipitating factor is treated, the rhythm reverts to baseline, coining the term Brugada Phenocopy. Here we present a captivating case of a 40-year-old female who was found unresponsive and determined to have a Brugada pattern on ECG secondary to hyperkalemia. Once appropriately treated, ECG reverts to normal baseline.

摘要

Brugada综合征是一种具有潜在致命性的遗传性心脏疾病,如果未被识别,可能会引发心源性猝死。心电图(ECG)显示右侧胸前导联出现特征性的穹窿样ST段抬高并伴有T波倒置,这是Brugada波型的特征性表现。最近有研究表明,某些异常情况,如电解质紊乱,可能会在心电图上诱发Brugada波型。一旦诱发因素得到治疗,心律就会恢复到基线水平,由此产生了“Brugada拟表型”这一术语。在此,我们呈现一例引人关注的病例,一名40岁女性被发现无反应,经检查因高钾血症导致心电图出现Brugada波型。经过适当治疗后,心电图恢复到正常基线水平。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a9aa/12118059/6ffe523cd80c/omaf036f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a9aa/12118059/f30ef9b6606d/omaf036f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a9aa/12118059/43e793fbb3aa/omaf036f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a9aa/12118059/6ffe523cd80c/omaf036f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a9aa/12118059/f30ef9b6606d/omaf036f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a9aa/12118059/43e793fbb3aa/omaf036f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a9aa/12118059/6ffe523cd80c/omaf036f3.jpg

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本文引用的文献

1
Brugada phenocopy secondary to hyperkalemia and hyponatremia in primary adrenal insufficiency.原发性肾上腺功能不全中继发于高钾血症和低钠血症的Brugada综合征拟表型。
J Am Coll Emerg Physicians Open. 2022 Aug 10;3(4):e12800. doi: 10.1002/emp2.12800. eCollection 2022 Aug.
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Brugada pattern as part of the electrocardiographic abnormalities in hyperkalemia.Brugada 波型是高钾血症心电图异常的一部分。
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Hyperkalemia mimicking brugada pattern in electrocardiogram: A rare case report from Nepal.
心电图中酷似 Brugada 图形的高钾血症:来自尼泊尔的罕见病例报告。
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Brugada Phenocopy Induced by Electrolyte Disorder: A Transient Electrocardiographic Sign.电解质紊乱诱发的Brugada波拟态:一种短暂的心电图表现
Ann Noninvasive Electrocardiol. 2016 Jul;21(4):429-32. doi: 10.1111/anec.12350. Epub 2016 Feb 23.
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New methodologies for measuring Brugada ECG patterns cannot differentiate the ECG pattern of Brugada syndrome from Brugada phenocopy.用于测量Brugada心电图模式的新方法无法区分Brugada综合征的心电图模式和Brugada表型模拟。
J Electrocardiol. 2016 Mar-Apr;49(2):187-91. doi: 10.1016/j.jelectrocard.2015.12.011. Epub 2015 Dec 23.
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Coronary anomalies and Brugada Phenocopy, the first documented case in the world.冠状动脉异常与Brugada表型模拟,世界首例文献记载病例。
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Brugada phenocopy: new terminology and proposed classification.Brugada综合征拟表型:新术语及拟分类
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Genetics of sudden cardiac death syndromes.致心律失常性右室心肌病、长 QT 综合征和 Brugada 综合征的遗传学
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9
The Brugada ECG pattern: a marker of channelopathy, structural heart disease, or neither? Toward a unifying mechanism of the Brugada syndrome.Brugada心电图模式:是离子通道病、结构性心脏病的标志物,还是两者皆非?迈向Brugada综合征的统一机制。
Circ Arrhythm Electrophysiol. 2010 Jun;3(3):283-90. doi: 10.1161/CIRCEP.110.937029.
10
The hyperkalemic Brugada sign.高钾血症性Brugada波征
J Electrocardiol. 2007 Jan;40(1):53-9. doi: 10.1016/j.jelectrocard.2006.10.057.