肺毛细血管血管瘤病

Pulmonary capillary hemangiomatosis.

作者信息

Magee F, Wright J L, Kay J M, Peretz D, Donevan R, Churg A

出版信息

Am Rev Respir Dis. 1985 Oct;132(4):922-5. doi: 10.1164/arrd.1985.132.4.922.

DOI:10.1164/arrd.1985.132.4.922

Abstract

We report a case of pulmonary capillary hemangiomatosis affecting a 35-yr-old Caucasian woman. Progressive pulmonary hypertension was documented by serial cardiac catheterizations, and pulmonary function studies showed changes suggestive of chronic pulmonary congestion. Although a difficult condition to diagnose during life as it may mimic veno-occlusive disease, capillary hemangiomatosis has a distinct histopathologic picture.

摘要

我们报告一例发生在一名35岁白人女性身上的肺毛细血管瘤病。通过连续的心导管检查记录到进行性肺动脉高压，肺功能研究显示出提示慢性肺淤血的变化。尽管毛细血管瘤病在生前很难诊断，因为它可能酷似静脉闭塞性疾病，但它有独特的组织病理学表现。