Dufour B, Maître S, Humbert M, Capron F, Simonneau G, Musset D
Service de Radiologie, Hôpital Antoine Béclère, Clamart, France.
AJR Am J Roentgenol. 1998 Nov;171(5):1321-4. doi: 10.2214/ajr.171.5.9798872.
Clinical differentiation of isolated pulmonary hypertensive arteriopathy from pulmonary capillary hemangiomatosis or pulmonary venoocclusive disease can be difficult on a clinical basis alone. Differentiation is important because misdiagnosis of pulmonary capillary hemangiomatosis or pulmonary venoocclusive disease may lead to severe vasodilator-induced pulmonary edema. The objective of our study was to determine whether high-resolution CT of the chest could distinguish pulmonary capillary hemangiomatosis or pulmonary venoocclusive disease from isolated pulmonary hypertensive arteriopathy.
Pulmonary hypertension in patients who also have pulmonary capillary hemangiomatosis or pulmonary venoocclusive disease shows characteristics on high-resolution CT that are not seen in patients with isolated pulmonary hypertensive arteriopathy.
仅基于临床情况，将孤立性肺动脉高压性动脉病与肺毛细血管瘤病或肺静脉闭塞病进行临床鉴别可能具有挑战性。鉴别很重要，因为肺毛细血管瘤病或肺静脉闭塞病的误诊可能导致严重的血管扩张剂诱发的肺水肿。我们研究的目的是确定胸部高分辨率CT是否能够将肺毛细血管瘤病或肺静脉闭塞病与孤立性肺动脉高压性动脉病区分开来。
同时患有肺毛细血管瘤病或肺静脉闭塞病的患者的肺动脉高压在高分辨率CT上呈现出孤立性肺动脉高压性动脉病患者所没有的特征。
