Edemskiy Alexander, Vasiltseva Oksana, Kliver Elena, Novikova Natalya, Sirota Dmitry, Chernyavskiy Alexander
Department of Aorta and Coronary Artery Surgery, E. Meshalkin National Medical Research Center, Ministry of Health of the Russian Federation, Novosibirsk, Russian Federation.
Braz J Cardiovasc Surg. 2025 Jun 18;40(4):e20230441. doi: 10.21470/1678-9741-2023-0441.
Pulmonary artery angiosarcoma is a rare and extremely severe tumor. Our study summarizes the clinical data of patients treated for pulmonary artery angiosarcoma over the period of 2010-2020.
We retrospectively analyzed cases of surgical treatment of patients with diagnosis of pulmonary artery angiosarcoma at our center. Data of operative findings, short-term follow-up, and the long-term results were reviewed where available.
The 30-day mortality rate was six (67%) out of nine patients. Three (33%) patients were discharged. Data on pulmonary vascular resistance in the earlyand long-term postoperative periods were assessed if possible. Certain computed tomography signs have been identified that can be used to suspect pulmonary artery angiosarcoma and make a differential diagnosis with chronic thromboembolic pulmonary hypertension.
The surgical treatment of choice is pneumonectomy with contralateral pulmonary endarterectomy. Oncological vigilance regarding angiosarcoma in occlusive-stenotic lesions of the pulmonary artery is extremely important. Patients' assessment must be carried out in an expert cardiothoracic surgery center with the involvement of an oncological crew.
肺动脉血管肉瘤是一种罕见且极为严重的肿瘤。我们的研究总结了2010年至2020年期间接受肺动脉血管肉瘤治疗的患者的临床数据。
我们回顾性分析了在本中心诊断为肺动脉血管肉瘤的患者的手术治疗病例。对手术所见、短期随访及长期结果的数据进行了回顾（如有可用数据）。
9例患者中有6例（67%）在30天内死亡。3例（33%）患者出院。术后早期和长期的肺血管阻力数据在可能的情况下进行了评估。已确定某些计算机断层扫描征象可用于怀疑肺动脉血管肉瘤并与慢性血栓栓塞性肺动脉高压进行鉴别诊断。
首选的手术治疗方法是肺切除术及对侧肺动脉内膜切除术。对肺动脉闭塞性狭窄病变中的血管肉瘤保持肿瘤学警惕极为重要。必须在有肿瘤学团队参与的专业心胸外科中心对患者进行评估。
