Reply to: "Comment on opinion paper on the diagnosis and treatment of progressive familial intrahepatic cholestasis".
作者信息
McKiernan Patrick, Bernabeu Jesus Quintero, Girard Muriel, Indolfi Giuseppe, Lurz Eberhard, Trivedi Palak
机构信息
Liver Unit and Small Bowel Transplantation, Birmingham Women's and Children's NHS Foundation Trust, Birmingham, UK.
Pediatric Hepatology and Liver Transplant Department, Hospital Universitari Vall d'Hebron, Barcelona, Spain.
出版信息
JHEP Rep. 2025 Mar 25;7(6):101402. doi: 10.1016/j.jhepr.2025.101402. eCollection 2025 Jun.
Abstract
摘要
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本文引用的文献
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EASL Clinical Practice Guidelines on genetic cholestatic liver diseases.EASL 临床实践指南：遗传性胆汁淤积性肝病。
J Hepatol. 2024 Aug;81(2):303-325. doi: 10.1016/j.jhep.2024.04.006. Epub 2024 Jun 8.
2
Opinion paper on the diagnosis and treatment of progressive familial intrahepatic cholestasis.关于进行性家族性肝内胆汁淤积症诊断与治疗的意见书
JHEP Rep. 2023 Oct 27;6(1):100949. doi: 10.1016/j.jhepr.2023.100949. eCollection 2024 Jan.
3
Outcomes of 38 patients with PFIC3: Impact of genotype and of response to ursodeoxycholic acid therapy.38例进行性家族性肝内胆汁淤积症3型患者的预后：基因型及对熊去氧胆酸治疗反应的影响
JHEP Rep. 2023 Jul 13;5(10):100844. doi: 10.1016/j.jhepr.2023.100844. eCollection 2023 Oct.
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