Flores-Costa Roger, Duran-Güell Marta, Romero-Grimaldo Berta, Contreras Bryan J, Salvatella Albert, Sánchez-Rodríguez María Belén, Uschner Frank, Klein Sabine, Diaz Alba, Huergo Estefanía, Gómez-Cabrero David, Bosch Jordi, Rautou Pierre-Emmanuel, Trebicka Jonel, López-Vicario Cristina, Clària Joan
Biochemistry and Molecular Genetics Service, Hospital Clínic-IDIBAPS and CIBERehd, Barcelona, Spain.
European Foundation for the Study of Chronic Liver Failure (EF CLIF) and Grifols Chair, Barcelona, Spain.
Hepatol Commun. 2025 Jun 19;9(7). doi: 10.1097/HC9.0000000000000744. eCollection 2025 Jul 1.
Acute-on-chronic liver failure (ACLF), which develops in patients with acutely decompensated cirrhosis, is characterized by multiple extrahepatic organ failures leading to high short-term mortality. Although major advances in the understanding of ACLF have been accomplished in the last years, the understanding of driving mechanisms underlying ACLF is hindered by the lack of proper animal models that faithfully reproduce both the systemic hyperinflammatory response and the full spectra of extrahepatic organ failures present in this condition.
ACLF was induced by acute induction of polymicrobial peritonitis secondary to the ligation and puncture of the cecum (CLP) in mice with chronic carbon tetrachloride (CCl4)-induced cirrhosis. The study included three groups: CCl4+CLP (n=10) mice with cirrhosis which underwent CLP surgery; CCl4+sham mice (n=10) and control mice (n=10).
As compared to CCl4+sham, CCl4+CLP mice had higher short-term mortality and exhibited more severe hypoalbuminemia and hyperbilirubinemia, significantly higher AST and GGT levels and higher liver inflammatory burden. CCl4+CLP mice also showed increased serum creatinine and BUN levels and up-regulated expression of Kim-1, Il-6 and Tnf in the kidney, lower oxygen saturation (SpO2), higher serum renin concentration, higher international normalized ratio (INR) and worse neurological behavior test scores than CCl4+sham and control mice. In addition, CCl4+CLP mice showed widespread bacterial tissue colonization and exhibited increased serum cytokine levels, which correlated with the intensity of organ impairments.
The CCl4+CLP model reproduces the full spectra of extrahepatic organ impairments present in patients with ACLF and represents an optimized murine model to experimentally explore the pathophysiology of this disease as well as new therapeutic approaches.
急性慢性肝衰竭(ACLF)发生于急性失代偿性肝硬化患者,其特征为多器官肝外功能衰竭,导致短期死亡率高。尽管近年来在ACLF的认识方面取得了重大进展,但由于缺乏能够忠实地再现全身高炎症反应以及该病症中存在的肝外器官功能衰竭全貌的合适动物模型,对ACLF潜在驱动机制的理解受到阻碍。
在慢性四氯化碳(CCl4)诱导肝硬化的小鼠中,通过结扎和穿刺盲肠(CLP)继发急性多微生物腹膜炎诱导ACLF。该研究包括三组:接受CLP手术的肝硬化CCl4 + CLP(n = 10)小鼠;CCl4 +假手术小鼠(n = 10)和对照小鼠(n = 10)。
与CCl4 +假手术组相比,CCl4 + CLP小鼠短期死亡率更高,表现出更严重的低白蛋白血症和高胆红素血症,AST和GGT水平显著更高,肝脏炎症负担更重。CCl4 + CLP小鼠还表现出血清肌酐和BUN水平升高,肾脏中Kim-1、Il-6和Tnf的表达上调,氧饱和度(SpO2)降低,血清肾素浓度升高,国际标准化比值(INR)更高,神经行为测试评分比CCl4 +假手术组和对照小鼠更差。此外,CCl4 + CLP小鼠表现出广泛的细菌组织定植,并表现出血清细胞因子水平升高,这与器官损伤的强度相关。
CCl4 + CLP模型再现了ACLF患者中存在的肝外器官损伤全貌,代表了一种优化的小鼠模型,用于实验性探索该疾病的病理生理学以及新的治疗方法。