Suppr超能文献

小鼠辐条蛋白3是纤毛中的一个代谢和调节中心。

Mouse radial spoke 3 is a metabolic and regulatory hub in cilia.

作者信息

Zhao Yanhe, Song Kangkang, Tavakoli Amirrasoul, Gui Long, Fernandez-Gonzalez Angeles, Zhang Song, Dzeja Petras P, Mitsialis S Alex, Zhang Xuewu, Nicastro Daniela

机构信息

Department of Cell Biology, University of Texas Southwestern Medical Center, Dallas, TX, USA.

Department of Biochemistry and Molecular Biotechnology and Cryo-Electron Microscopy Core Facility, University of Massachusetts Chan Medical School, Worcester, MA, USA.

出版信息

Nat Struct Mol Biol. 2025 Jun 27. doi: 10.1038/s41594-025-01594-6.

Abstract

Cilia are microtubule-based organelles that have important roles in cell sensing, signaling and motility. Recent studies have revealed the atomic structures of many multicomponent ciliary complexes, elucidating their mechanisms of action. However, little is known about the structure, proteome and function of full-length radial spoke 3 (RS3), a conserved complex that transmits mechanochemical signals to coordinate ciliary motility. Here, we combined single-particle cryo-electron microscopy, cryo-electron tomography, proteomic analysis and computational modeling to determine the three-dimensional structure and atomic model of RS3 from mouse respiratory cilia. We reveal all RS3 components, including regulatory and metabolic enzymes such as a protein kinase A subunit, adenylate kinases (AKs) and malate dehydrogenases. Furthermore, we confirm RS3 loss in AK7-deficient mice, which exhibit motility defects. Our findings identify RS3 as an important regulatory and metabolic hub that maintains sufficient adenosine triphosphate for sustained ciliary beating, providing insights into the etiology of ciliopathies.

摘要

纤毛是以微管为基础的细胞器,在细胞感知、信号传导和运动中发挥着重要作用。最近的研究揭示了许多多组分纤毛复合体的原子结构,阐明了它们的作用机制。然而,对于全长径向辐条3(RS3)的结构、蛋白质组和功能却知之甚少,RS3是一种保守的复合体,可传递机械化学信号以协调纤毛运动。在这里,我们结合单颗粒冷冻电子显微镜、冷冻电子断层扫描、蛋白质组分析和计算建模,来确定小鼠呼吸道纤毛中RS3的三维结构和原子模型。我们揭示了所有RS3组分,包括调节酶和代谢酶,如蛋白激酶A亚基、腺苷酸激酶(AKs)和苹果酸脱氢酶。此外,我们证实了AK7缺陷小鼠中RS3的缺失,这些小鼠表现出运动缺陷。我们的研究结果确定RS3是一个重要的调节和代谢中心,它能维持足够的三磷酸腺苷以支持纤毛持续跳动,为纤毛病的病因学提供了见解。

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验