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保守修复方法在一名10岁低汗型外胚层发育不良患儿修复治疗中的应用

Application of a Conservative Prosthodontic Approach in the Rehabilitation of a 10-Year-Old Child with Hypohidrotic Ectodermal Dysplasia.

作者信息

Alazmah Abdulfatah

机构信息

Department of Pediatric Dentistry, College of Dentistry, Prince Sattam bin Abdulaziz University, Al-Kharj 11942, Saudi Arabia.

出版信息

Healthcare (Basel). 2025 Jun 28;13(13):1543. doi: 10.3390/healthcare13131543.

DOI:10.3390/healthcare13131543
PMID:40648568
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12249313/
Abstract

: Hypohidrotic ectodermal dysplasia (HED) is a rare hereditary disorder affecting ectoderm-derived tissues including teeth, hair, and sweat glands. The dental abnormalities associated with HED, such as oligodontia and conical teeth, often result in significant functional, esthetic, and psychosocial challenges, particularly during childhood. : A 10-year-old child presented with psychosocial concerns related to missing and malformed teeth. Clinical examination revealed oligodontia, conical anterior teeth, and a resorbed mandibular ridge. Based on clinical findings and a positive family history, a diagnosis of HED with significant dental involvement was confirmed. : A conservative prosthodontic approach was selected. A maxillary overdenture was fabricated over the retained primary teeth to enhance retention and preserve the alveolar bone, and a resin-bonded bridge was placed in the mandible due to poor ridge anatomy. The treatment restored oral function and esthetics and improved the child's self-esteem. A recall visit after three months confirmed good prosthesis adaptation and a positive response from the patient and parents. : This case highlights the importance of early, conservative, and developmentally appropriate prosthetic rehabilitation in pediatric patients with HED. Interim prostheses can significantly improve oral function, appearance, and psychosocial well-being while preserving future treatment options as the child matures.

摘要

少汗性外胚层发育不良(HED)是一种罕见的遗传性疾病,会影响外胚层衍生组织,包括牙齿、头发和汗腺。与HED相关的牙齿异常,如少牙症和锥形牙,常常会导致严重的功能、美观和心理社会挑战,尤其是在儿童时期。

一名10岁儿童因牙齿缺失和畸形而出现心理社会问题。临床检查发现少牙症、锥形前牙和下颌牙槽嵴吸收。根据临床发现和阳性家族史,确诊为伴有严重牙齿受累的HED。

选择了保守的修复方法。在保留的乳牙上制作上颌覆盖义齿以增强固位并保留牙槽骨,由于牙槽嵴解剖结构不佳,在下颌放置了树脂粘结桥。治疗恢复了口腔功能和美观,提高了患儿的自尊心。三个月后的复诊确认义齿适配良好,患者及家长反应积极。

该病例强调了对患有HED的儿科患者进行早期、保守且适合发育阶段的修复康复的重要性。临时修复体可显著改善口腔功能、外观和心理社会幸福感,同时在患儿成长过程中保留未来的治疗选择。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/048ecc193e0a/healthcare-13-01543-g009.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/e6c360c025e2/healthcare-13-01543-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/c448ba2d69f1/healthcare-13-01543-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/d8ea8d6a1fc4/healthcare-13-01543-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/82e26ecdef39/healthcare-13-01543-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/3f8257693010/healthcare-13-01543-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/2664228b29c4/healthcare-13-01543-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/375c70e2a0a9/healthcare-13-01543-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/8aac236792bb/healthcare-13-01543-g008.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/048ecc193e0a/healthcare-13-01543-g009.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/e6c360c025e2/healthcare-13-01543-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/c448ba2d69f1/healthcare-13-01543-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/d8ea8d6a1fc4/healthcare-13-01543-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/82e26ecdef39/healthcare-13-01543-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/3f8257693010/healthcare-13-01543-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/2664228b29c4/healthcare-13-01543-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/375c70e2a0a9/healthcare-13-01543-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/8aac236792bb/healthcare-13-01543-g008.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4e1d/12249313/048ecc193e0a/healthcare-13-01543-g009.jpg

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本文引用的文献

1
Dental Implants as a Treatment Option for Prosthetic Rehabilitation of Children with Ectodermal Dysplasia: A Systematic Review.牙种植体作为外胚层发育不全儿童修复性康复的一种治疗选择:一项系统评价
Int J Clin Pediatr Dent. 2025 Mar;18(3):339-347. doi: 10.5005/jp-journals-10005-3069. Epub 2025 Apr 19.
2
Dental Management of Genetic Dental Disorders: A Critical Review.遗传性牙病的口腔治疗管理:一项批判性综述
J Dent Res. 2025 Apr;104(4):369-379. doi: 10.1177/00220345241305330. Epub 2025 Feb 4.
3
Developmental and Acquired Abnormalities of the Teeth.
牙齿的发育性和获得性异常。
Dent Clin North Am. 2024 Apr;68(2):227-245. doi: 10.1016/j.cden.2023.09.001. Epub 2023 Oct 29.
4
Prosthetic rehabilitation of a patient with ectrodactyly-ectodermal dysplasia-cleft lip/palate syndrome through a hybrid workflow: A case report with 2-year follow-up.通过混合工作流程对外胚层发育不良-外胚层发育不良-唇腭裂综合征患者进行假体修复:2 年随访的病例报告。
Spec Care Dentist. 2024 Jan-Feb;44(1):96-102. doi: 10.1111/scd.12826. Epub 2023 Jan 18.
5
Rehabilitation Considerations for Very Young Children with Severe Oligodontia due to Ectodermal Dysplasia: Report of Three Clinical Cases with a 2-Year Follow-Up.外胚层发育不良所致严重少牙畸形幼儿的康复考量:三例临床病例报告及两年随访
Case Rep Dent. 2022 Mar 22;2022:9925475. doi: 10.1155/2022/9925475. eCollection 2022.
6
Early prosthodontic intervention on two three-year-old twin girls with ectodermal dysplasia.对两名三岁患有外胚层发育不良的双胞胎女孩进行早期修复干预。
Eur J Paediatr Dent. 2019 Jun;20(2):139-142. doi: 10.23804/ejpd.2019.20.02.11.
7
Ectodermal dysplasias: Classification and organization by phenotype, genotype and molecular pathway.外胚层发育不全:按表型、基因型和分子途径分类和组织。
Am J Med Genet A. 2019 Mar;179(3):442-447. doi: 10.1002/ajmg.a.61045. Epub 2019 Jan 31.
8
Prosthetic rehabilitation of patients with hypohidrotic ectodermal dysplasia: A systematic review.少汗型外胚层发育不良患者的假体康复:一项系统评价。
J Oral Rehabil. 2018 Jul;45(7):555-570. doi: 10.1111/joor.12638. Epub 2018 May 9.
9
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J Oral Rehabil. 2016 May;43(5):373-87. doi: 10.1111/joor.12384. Epub 2016 Feb 22.
10
Rehabilitation of children with ectodermal dysplasia. Part 1: an international Delphi study.儿童外胚层发育不良的康复。第 1 部分:国际德尔菲研究。
Int J Oral Maxillofac Implants. 2013 Jul-Aug;28(4):1090-100. doi: 10.11607/jomi.2980.