Department of Paediatric Dentistry, Chang-Gung Memorial Hospital, Taoyuan, Taiwan.
Eur J Paediatr Dent. 2019 Jun;20(2):139-142. doi: 10.23804/ejpd.2019.20.02.11.
Early prosthodontic treatment for cases of ectodermal dysplasia (ED) is usually difficult because of oligodontia, undeveloped alveolar ridges, and the young age of the patients. Although some cases of prosthetic management of ED patients have been reported in the literature, there have been few cases about prosthetic treatment in children younger than 5 years of age.
This case report presents early prosthetic oral rehabilitation of 2 twin sisters with ectodermal dysplasia and severe hypodontia in the primary dentition. Fixed partial dentures with bands retained on deciduous molars were fabricated when the girls were 3 years old. New flexible removable partial dentures were made when the girls turned 6 years to accommodate the ongoing alveolar development. After the dental treatment, the two girls' aesthetics, phonetics, and chewing functions all improved significantly, which in turn raised the girls' self-esteem and increased their overall quality of life.
These two cases demonstrated that properly timed and managed early prosthodontic intervention can improve the overall life quality of young patients with ectodermal dysplasia.
由于牙列稀疏、牙槽嵴发育不良以及患者年龄较小，牙体外胚层发育不全（ED）患者的早期修复治疗通常较为困难。尽管文献中有一些关于 ED 患者修复治疗的病例报道，但关于 5 岁以下儿童修复治疗的病例却很少。
本病例报告介绍了一对牙列严重缺失的 ED 双胞胎姐妹的早期口腔修复治疗情况。当女孩们 3 岁时，制作了带有固位带的固定局部义齿修复乳牙。当女孩们 6 岁时，为了适应正在进行的牙槽骨发育，制作了新的弹性可摘局部义齿。经过牙科治疗，两个女孩的美观、语音和咀嚼功能都有了显著改善，从而提高了女孩们的自尊心，提高了她们的整体生活质量。
这两个病例表明，适时、合理的早期修复干预可以提高牙体外胚层发育不全年轻患者的整体生活质量。
