Nagarajan Divyashri R, Mani Jacob Daya, Ottu Para Niyas Khalid
Internal Medicine, Burjeel Medical City, Abu Dhabi, ARE.
Cureus. 2025 Jul 23;17(7):e88574. doi: 10.7759/cureus.88574. eCollection 2025 Jul.
Autoimmune polyglandular syndrome type 3 (APS type 3) is defined by the coexistence of autoimmune thyroid disease with other autoimmune disorders, excluding adrenal insufficiency. It is a common but often under-recognized entity, particularly in young women with multiple autoimmune conditions. We report the case of a 27-year-old woman with a longstanding history of type 1 diabetes mellitus (T1DM) who presented with multiple episodes of diabetic ketoacidosis to the emergency department. She presented with fatigue and had poor glycemic control (HbA1c 11.3%). She was further diagnosed in the ward with refractory autoimmune hypothyroidism, pernicious anemia, celiac disease with poor dietary adherence, and proliferative diabetic retinopathy requiring retinal intervention. Physical examinations, blood workup, and radiological investigations revealed no signs of adrenal insufficiency or pituitary adenoma. The combination of autoimmune thyroid disease, T1DM, pernicious anemia, celiac disease, and systemic autoimmunity, in the absence of adrenal involvement, is consistent with a diagnosis of APS type 3 with overlapping subtypes. This case illustrates the clinical complexity and diagnostic challenges of APS type 3. Early identification and multidisciplinary management of coexisting autoimmune disorders are essential for improving long-term outcomes and reducing complications. Attention to dietary adherence, appropriate thyroid hormone dosing, and ongoing screening for evolving autoimmune involvement are critical elements in the care of such patients.
3型自身免疫性多腺体综合征(APS 3型)的定义是自身免疫性甲状腺疾病与其他自身免疫性疾病并存,但不包括肾上腺功能不全。它是一种常见但常未被认识的疾病,在患有多种自身免疫性疾病的年轻女性中尤为如此。我们报告了一例27岁1型糖尿病(T1DM)病史较长的女性病例,该患者因多次糖尿病酮症酸中毒发作就诊于急诊科。她表现为疲劳,血糖控制不佳(糖化血红蛋白HbA1c为11.3%)。在病房进一步诊断为难治性自身免疫性甲状腺功能减退、恶性贫血、饮食依从性差的乳糜泻以及需要视网膜干预的增殖性糖尿病视网膜病变。体格检查、血液检查和影像学检查均未发现肾上腺功能不全或垂体腺瘤的迹象。在无肾上腺受累的情况下,自身免疫性甲状腺疾病、T1DM、恶性贫血、乳糜泻和全身自身免疫性疾病的组合符合伴有重叠亚型的APS 3型诊断。该病例说明了APS 3型的临床复杂性和诊断挑战。早期识别和对并存自身免疫性疾病的多学科管理对于改善长期预后和减少并发症至关重要。注意饮食依从性、适当的甲状腺激素剂量以及持续筛查不断演变的自身免疫性受累情况是此类患者护理中的关键要素。