Iwai N, Yanagihara J, Tsuto T, Taniguchi H, Takahashi T
Z Kinderchir. 1985 Dec;40(6):371-3. doi: 10.1055/s-2008-1059753.
A 1-day-old male infant with congenital short small bowel was transferred to our hospital because of bilious vomiting and abdominal distension. An exploratory laparotomy performed at the age of 8 days revealed malrotation without any volvulus or stenosis of the small intestine, which was 45 cm long. There were no other anomalies except absence of the appendix. Postoperative nutritional support was by intravenous hyperalimentation and administration of elemental diet. However, parenteral nutrition was discontinued because of hyperbilirubinaemia. The patient died from marked emaciation at 2 months of age despite the administration of elemental diet. Therefore, careful total parenteral nutrition is the only management for successful therapy until the child's intestinal absorptive function develops.
一名患有先天性短小肠的1日龄男婴因胆汁性呕吐和腹胀被转至我院。8日龄时进行的剖腹探查术显示存在肠旋转不良，小肠无扭转或狭窄，小肠长度为45厘米。除阑尾缺如外无其他异常。术后营养支持采用静脉高营养和给予要素饮食。然而，由于高胆红素血症，肠外营养被停用。尽管给予了要素饮食，该患儿仍在2月龄时因极度消瘦死亡。因此，在儿童肠道吸收功能发育之前，谨慎的全肠外营养是成功治疗的唯一管理方法。
