Postuma R, Moroz S, Friesen F
J Pediatr Surg. 1983 Jun;18(3):264-8. doi: 10.1016/s0022-3468(83)80096-7.
This full term male infant required a 90% enterectomy for congenital intestinal volvulus shortly after birth. The remaining small bowel consisted of 8 cm of proximal jejunum anastomosed to 5 cm of terminal ileum. The ileocecal valve was intact. Parenteral nutrition was administered for the first 21 months, including 17 months of home parenteral nutrition. The child's oral diet was mother's milk until 28 months of age when he was switched to an elemental diet. Solids were introduced at 6 months of age. Presently, at 36 months of age, the infant is off parenteral nutrition and is maintaining good nutritional status on a diet of 150 calories per kilo per day. His major problem has been an extreme allergy to cow's-milk protein. This infant is remarkable, since, despite record short bowel length, he maintained a completely normal growth and development, had remarkably few serious complications, spent relatively little time in hospital, and has documented improvement of G.I. absorption and radiographic contrast studies.
这名足月男婴出生后不久因先天性肠扭转接受了90%的肠切除术。剩余的小肠由8厘米近端空肠与5厘米末端回肠吻合而成。回盲瓣完整。在最初的21个月里给予肠外营养，其中包括17个月的家庭肠外营养。孩子一直母乳喂养至28个月大，之后改为要素饮食。6个月大时开始添加固体食物。目前，在36个月大时，该婴儿已停用肠外营养，每天每公斤摄入150卡路里的饮食，营养状况良好。他的主要问题是对牛奶蛋白极度过敏。这名婴儿很了不起，因为尽管肠管长度创纪录地短，但他保持了完全正常的生长发育，严重并发症极少，住院时间相对较短，并且有证据表明胃肠道吸收和影像学造影检查有所改善。
