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2015 - 2023年瑞典新生儿干血斑筛查诊断检查中的下一代测序技术

Next-Generation Sequencing in the Diagnostic Workup of Neonatal Dried Blood Spot Screening in Sweden 2015-2023.

作者信息

Sörensen Lene, Asin-Cayuela Jorge, Barbaro Michela, Bruhn Helene, Engvall Martin, Lesko Nicole, Naess Karin, Oscarson Mikael, Shen Yan, Ueberschär Malin, Wredenberg Anna, Sterky Fredrik H, Wedell Anna, Zetterström Rolf H

机构信息

Centre for Inherited Metabolic Diseases, Karolinska University Hospital Solna, 171 76 Stockholm, Sweden.

Department of Molecular Medicine and Surgery, Karolinska Institutet, 171 77 Stockholm, Sweden.

出版信息

Int J Neonatal Screen. 2025 Sep 3;11(3):73. doi: 10.3390/ijns11030073.

Abstract

Sweden has one neonatal screening laboratory and two centers conducting diagnostic workup for inborn errors of metabolism (IEM). Next-generation sequencing (NGS) has been gradually introduced as a confirmatory diagnostic test in the Swedish newborn screening program. Here, we describe the use of NGS in the diagnostic workup of IEM in screening-detected babies in Sweden between 2015 and 2023. During this period, 1,023,344 newborn children were screened, and 81 of 290 IEM cases were genetically confirmed using NGS. Planned improvements to the program are to perform genetic validation directly on the initial dried blood spot (DBS). As whole-genome sequencing (WGS) is superior in detecting causative genetic variants compared to Sanger sequencing, targeted NGS, and whole-exome sequencing (WES), it will likely become the method of choice more broadly in the future. A strong focus is to consolidate the nationally coordinated DBS newborn screening program, with all its individual components, including screening, targeted diagnostics, individualized treatment, and follow-up. This challenges the current regionalized organization of Swedish healthcare, which hinders close national collaboration between experts and sharing of data, as well as equal access to advanced treatments for identified patients, regardless of their place of birth.

摘要

瑞典有一个新生儿筛查实验室和两个开展先天性代谢缺陷病(IEM)诊断检查的中心。下一代测序(NGS)已在瑞典新生儿筛查项目中逐渐作为一种确诊诊断测试被引入。在此,我们描述了2015年至2023年期间NGS在瑞典筛查发现的患有IEM的婴儿诊断检查中的应用。在此期间,对1,023,344名新生儿进行了筛查,290例IEM病例中有81例通过NGS得到基因确诊。该项目计划的改进措施是直接在初始干血斑(DBS)上进行基因验证。由于与桑格测序、靶向NGS和全外显子测序(WES)相比,全基因组测序(WGS)在检测致病基因变异方面更具优势,它未来可能会更广泛地成为首选方法。一个重点是巩固全国协调的DBS新生儿筛查项目及其所有单独组成部分,包括筛查、靶向诊断、个体化治疗和随访。这对瑞典医疗保健当前的区域化组织构成了挑战,这种区域化组织阻碍了专家之间紧密的国家合作和数据共享,以及确诊患者无论出生地如何都能平等获得先进治疗。

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Genomic newborn screening for rare diseases.针对罕见病的基因组新生儿筛查。
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