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[良性慢性结合胆红素血症:罗特综合征还是肝储存功能受损?]

[Benign chronic conjugated hyperbilirubinaemia: rotor syndrome or hepatic storage impairment?].

作者信息

Knoflach P, Horak W, Kerstan E, Thaler H

出版信息

Z Gastroenterol. 1979 Jan;17(1):32-7.

PMID:419795
Abstract

In a 52-year-old female who was jaundiced since early childhood, marked conjugated hyperbilirubinaemia and a delay of bromsulfophthalein and indocyanine green plasma disappearance rates were observed. Liver histology, plasma bile acids and plasma clearance of 14-C-cholic acid were normal. There was a pronounced impairment of the relative storage capacity of bromsulfophthalein (S = 2,4 mg/mg%) and a moderate decrease of BSP-transport maximum.

摘要

在一名自幼儿期起就出现黄疸的52岁女性患者中,观察到明显的结合胆红素血症以及溴磺酞钠和吲哚菁绿血浆消失率延迟。肝脏组织学、血浆胆汁酸和14-C-胆酸的血浆清除率均正常。溴磺酞钠的相对储存能力明显受损(S = 2.4 mg/mg%),且溴磺酞钠转运最大值有中度降低。

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