Knudson R P, Alden E R
Pediatrics. 1979 Aug;64(2):238-41.
The symptomatology and sequelae of symptomatic system arteriovenous (A-V) malformations in children less than 6 months old make an early diagnosis possible and early treatment mandatory. A group of 156 infants with systemic A-V malformations involving the CNS (81 infants), liver (61 infants), and lungs (14 infants) were studied to compare symptoms, diagnosis, treatment, and outcome. Congestive heart failure was present in 67% of the patients with CNS A-V malformations. Mortality among the patients with CNS A-V fistulas was 64%. Of those patients with hepatic A-V malformations 67% had abdominal masses, 48% congestive heart failure, and 55% died. Pulmonary A-V malformations presented with congestive heart failure 57%, cyanosis 43%, and resulted in a 43% mortality. Early combined medical and surgical therapy offered the best chance for a successful outcome.
6个月以下儿童症状性系统性动静脉(A-V)畸形的症状和后遗症使得早期诊断成为可能,早期治疗成为必需。对一组156例患有累及中枢神经系统(81例婴儿)、肝脏(61例婴儿)和肺部(14例婴儿)的系统性A-V畸形的婴儿进行了研究,以比较症状、诊断、治疗和结果。中枢神经系统A-V畸形患者中67%出现充血性心力衰竭。中枢神经系统A-V瘘患者的死亡率为64%。患有肝A-V畸形的患者中,67%有腹部肿块,48%有充血性心力衰竭,55%死亡。肺A-V畸形患者出现充血性心力衰竭的比例为57%,发绀的比例为43%,死亡率为43%。早期联合药物和手术治疗为成功治疗提供了最佳机会。