姐妹中的“红细胞生成性”原卟啉症与肝硬化
'Erythropoietic' protoporphyria and cirrhosis in sisters.
作者信息
Thompson R P, Molland E A, Nicholson D C, Gray C H
出版信息
Gut. 1973 Dec;14(12):934-8. doi: 10.1136/gut.14.12.934.
Abstract
The clinical and histopathological features of two sisters with erythropoietic protoporphyria and liver disease are described. They had unusually severe photosensitivity with blistering, and both died at the age of 31 from cirrhosis. The association of erythropoietic protoporphyria with several hepatic abnormalities is discussed.
摘要
描述了两名患有红细胞生成性原卟啉症和肝病的姐妹的临床和组织病理学特征。她们有异常严重的光敏性并伴有水疱形成，两人均在31岁时死于肝硬化。讨论了红细胞生成性原卟啉症与几种肝脏异常的关联。
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