Branching enzyme-deficiency glycogenosis: studies in therapy.
作者信息
Fernandes J, Huijing F
出版信息
Arch Dis Child. 1968 Jun;43(229):347-52. doi: 10.1136/adc.43.229.347.
Abstract
摘要
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Pediatrics. 1965 Mar;35:470-7.
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AN ELECTRON MICROSCOPIC AND BIOCHEMICAL STUDY OF TYPE II GLYCOGENOSIS.II型糖原贮积病的电子显微镜及生化研究
Lab Invest. 1964 Sep;13:1139-52.
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Type IV glycogenosis. Report of a case proven by characterization of glycogen and studied at necropsy.IV型糖原贮积病。一例经糖原特征鉴定并经尸检研究证实的病例报告。
Bull Johns Hopkins Hosp. 1962 Sep;111:157-81.
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One-second needle biopsy of the liver.肝脏一秒针穿刺活检
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Familial cirrhosis of the liver with storage of abnormal glycogen.伴有异常糖原储存的家族性肝硬化
Lab Invest. 1956 Jan-Feb;5(1):11-20.
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Biochemical studies on branched-chain oxoacid oxidases.支链氧代酸氧化酶的生化研究
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Effect of glucamylase on tissue glycogen and tissue glucamylase in the rat.葡糖淀粉酶对大鼠组织糖原及组织葡糖淀粉酶的影响。
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