The formation of propionate from the side-chain of cholesterol in an infant with an inborn error in the metabolism of propionate.
作者信息
Mitropoulos K A, Myant N B, Gompertz D
出版信息
Biochem J. 1970 Jul;118(3):551-2. doi: 10.1042/bj1180551.
Abstract
摘要
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The formation of propionate from the side-chain of cholesterol in an infant with an inborn error in the metabolism of propionate.在一名患有丙酸代谢先天性缺陷的婴儿中，由胆固醇侧链形成丙酸。
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The metabolism of cholesterol in the presence of liver mitochondria from normal and thyroxine-treated rats.正常大鼠和经甲状腺素处理的大鼠肝脏线粒体存在时胆固醇的代谢
Biochem J. 1965 Mar;94(3):594-603. doi: 10.1042/bj0940594.
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Catabolism of 2-methyloctanoic acid and 3beta-hydroxycholest-5-en-26-oic acid.2-甲基辛酸和 3β-羟基胆甾-5-烯-26-酸的分解代谢。
Biochem J. 1966 Dec;101(3):632-5. doi: 10.1042/bj1010632.
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