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Purification and properties of pyruvate kinase in normal and in pyruvate kinase deficient human red blood cells.

作者信息

Blume K G, Hoffbauer R W, Busch D, Arnold H, Löhr G W

出版信息

Biochim Biophys Acta. 1971 Feb 10;227(2):364-72. doi: 10.1016/0005-2744(71)90068-4.

DOI:10.1016/0005-2744(71)90068-4
PMID:5550823
Abstract
摘要

相似文献

1
Purification and properties of pyruvate kinase in normal and in pyruvate kinase deficient human red blood cells.正常及丙酮酸激酶缺乏的人红细胞中丙酮酸激酶的纯化及性质
Biochim Biophys Acta. 1971 Feb 10;227(2):364-72. doi: 10.1016/0005-2744(71)90068-4.
2
Mechanism of fructose diphosphate activation of a mutant pyruvate kinase from human red cells.果糖二磷酸对人红细胞突变型丙酮酸激酶的激活机制。
Biochim Biophys Acta. 1970 Apr 22;206(1):87-97. doi: 10.1016/0005-2744(70)90085-9.
3
[Anomalies of glycolysis during hemolytic anemia due to deficiency of pyruvate kinase in the erythrocytes].红细胞丙酮酸激酶缺乏所致溶血性贫血时糖酵解异常
Clin Chim Acta. 1968 Oct;22(2):165-81. doi: 10.1016/0009-8981(68)90354-9.
4
Studies on pyruvate kinase (PK) deficiency. II. Electrophoretic, kinetic and immunological studies on pyruvate kinase of erythrocytes and other tissues.
J Biochem. 1973 Dec;74(6):1165-75. doi: 10.1093/oxfordjournals.jbchem.a130344.
5
Atypical pyruvate kinase in a patient with haemolytic anaemia.一名溶血性贫血患者的非典型丙酮酸激酶
Scand J Haematol. 1971;8(2):126-33. doi: 10.1111/j.1600-0609.1971.tb01963.x.
6
[Congenital pyruvate kinase deficiency in erythrocytes: kinetic study of the enzyme and metabolic consequences].
Clin Chim Acta. 1972 Apr;38(1):131-40. doi: 10.1016/0009-8981(72)90218-5.
7
The molecular heterogeneity of red cell enzymopathies.
Isr J Med Sci. 1973 Sep-Oct;9(9):1361-4.
8
[Erythrocyte and leucocyte 3-phosphoglycerate kinase deficiency. Studies of properties of the enzyme, phagocytic activity of the polymorphonuclear leucoytes and a review of the literature].
Nouv Rev Fr Hematol. 1974 Jul-Aug;14(4):495-508.
9
[Erythrocytic pyruvate kinase. II. Enzymatic heterogeneity of deficiencies. Studies concerning 28 cases with congenital hemolytic anemia].[红细胞丙酮酸激酶。II. 缺乏症的酶学异质性。关于28例先天性溶血性贫血的研究]
Nouv Rev Fr Hematol. 1972 Sep-Oct;12(5):569-94.
10
[A case of nonspherocytic hemolytic anemia caused by deficient activity of erythrocyte pyruvate kinase].
Probl Gematol Pereliv Krovi. 1971 Oct;16(10):58-60.

引用本文的文献

1
Advances in Red Blood Cells Research.红细胞研究进展。
Cells. 2024 Feb 18;13(4):359. doi: 10.3390/cells13040359.
2
Pyruvate kinase, a possible regulatory enzyme in higher plants.丙酮酸激酶,高等植物中一种可能的调节酶。
Plant Physiol. 1973 Oct;52(4):312-7. doi: 10.1104/pp.52.4.312.
3
Hereditary erythrocyte pyruvate-kinase (PK) deficiency and chronic hemolytic anemia: clinical, genetic and molecular studies in six new Spanish patients.遗传性红细胞丙酮酸激酶(PK)缺乏症与慢性溶血性贫血:对6名西班牙新患者的临床、遗传及分子研究
Hum Genet. 1980;53(3):401-8. doi: 10.1007/BF00287063.
4
Purification and characterization of orotidine-5'-phosphate decarboxylase from Escherichia coli K-12.来自大肠杆菌K-12的乳清苷-5'-磷酸脱羧酶的纯化与特性分析
J Bacteriol. 1983 Nov;156(2):620-4. doi: 10.1128/jb.156.2.620-624.1983.
5
[Hemolytic anemia in Wilson's disease (hepato-lenticular degeneration)].[威尔逊病(肝豆状核变性)中的溶血性贫血]
Klin Wochenschr. 1972 Nov 1;50(21):995-1002. doi: 10.1007/BF01486994.
6
Erythrocyte enzyme deficiencies. Pyruvate kinase deficiency.红细胞酶缺乏症。丙酮酸激酶缺乏症。
J Clin Pathol Suppl (R Coll Pathol). 1974;8:128-33.
7
Pyruvate kinase isozymes in man. II. L type and erythrocyte-type isozymes. Electrofocusing and immunologic studies.人类丙酮酸激酶同工酶。II. L型和红细胞型同工酶。等电聚焦和免疫学研究。
Hum Genet. 1976 Jul 7;33(1):35-46. doi: 10.1007/BF00447284.
8
Molecular mechanism of erythrocyte pyruvate kinase deficiency.红细胞丙酮酸激酶缺乏症的分子机制
Humangenetik. 1975 Oct 7;29(4):271-80. doi: 10.1007/BF00394188.
9
Interaction of pigeon-liver nicotinamide-adenine dinucleotide kinase with cibacron blue F3GA.鸽肝烟酰胺腺嘌呤二核苷酸激酶与汽巴克隆蓝F3GA的相互作用。
Biochem J. 1976 Nov;159(2):441-3. doi: 10.1042/bj1590441.
10
[Enzyme deficiencies in glycolysis and nucleotide metabolism of red blood cells in nonspherocytic hemolytic anemia (author's transl)].非球形红细胞性溶血性贫血中红细胞糖酵解及核苷酸代谢的酶缺乏(作者译)
Klin Wochenschr. 1976 Sep 1;54(17):803-21. doi: 10.1007/BF01469302.