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原发性肺内神经源性肉瘤伴肥厚性肺骨关节病和石棉沉着病。

Primary intrapulmonary neurogenic sarcoma with hypertrophic pulmonary osteoarthropathy and asbestosis.

作者信息

Caves P K, Jacques J

出版信息

Thorax. 1971 Mar;26(2):212-8. doi: 10.1136/thx.26.2.212.

DOI:10.1136/thx.26.2.212
PMID:5576539
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1019129/
Abstract

A case of primary intrapulmonary neurogenic sarcoma with hypertrophic pulmonary osteoarthropathy and asbestosis is described. The essential histological features of this rare tumour are detailed, and the five authentic cases previously reported are reviewed. The pathogenesis of hypertrophic pulmonary osteoarthropathy and its occurrence in this case are discussed. After surgical removal of the tumour recurrence appeared in the chest within six months. It responded poorly to radiotherapy, and death from metastases occurred 16 months after operation.

摘要

本文描述了一例伴有肥厚性肺骨关节病和石棉沉着病的原发性肺内神经源性肉瘤病例。详细阐述了这种罕见肿瘤的基本组织学特征,并回顾了此前报道的五例真实病例。讨论了肥厚性肺骨关节病的发病机制及其在该病例中的发生情况。肿瘤手术切除后六个月内胸部出现复发。其对放疗反应不佳,术后16个月因转移而死亡。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/5ff6d4acde21/thorax00116-0080-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/07565ba384c8/thorax00116-0079-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/d737f6fbd6f9/thorax00116-0079-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/2d7f9896f276/thorax00116-0079-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/ff1de23df25b/thorax00116-0077-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/2584af033b7e/thorax00116-0078-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/5ff6d4acde21/thorax00116-0080-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/07565ba384c8/thorax00116-0079-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/d737f6fbd6f9/thorax00116-0079-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/2d7f9896f276/thorax00116-0079-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/ff1de23df25b/thorax00116-0077-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/2584af033b7e/thorax00116-0078-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/54e3/1019129/5ff6d4acde21/thorax00116-0080-a.jpg

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Sci Rep. 2020 Feb 19;10(1):2915. doi: 10.1038/s41598-020-59735-4.
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[Neurogenic sarcoma of the head and neck with contact to the skull base (author's transl)].头颈部神经源性肉瘤累及颅底(作者译)
Arch Otorhinolaryngol. 1981;233(3):271-300. doi: 10.1007/BF00454391.

本文引用的文献

1
Hyaline and calcified pleural plaques as an index of exposure to asbestos.透明性和钙化性胸膜斑作为石棉暴露的指标。
Br Med J. 1966 Apr 30;1(5495):1069-74. doi: 10.1136/bmj.1.5495.1069.
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Primary solitary neurogenic tumors of the lung.原发性肺孤立性神经源性肿瘤
J Thorac Surg. 1951 Feb;21(2):194-201.
3
Generalized hypertrophic osteoarthropathy in association with bronchial carcinoma; a review, based on 24 cases.与支气管癌相关的全身性肥大性骨关节病;基于24例病例的综述
Br Med J. 1955 Mar 26;1(4916):754-9. doi: 10.1136/bmj.1.4916.754.
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INTRAPULMONARY NEUROGENIC TUMORS.肺内神经源性肿瘤
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DIFFUSE MESOTHELIOMA OF THE PLEURA AND ASBESTOS.胸膜弥漫性间皮瘤与石棉
Br Med J. 1965 Feb 6;1(5431):350-3. doi: 10.1136/bmj.1.5431.350.
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PULMONARY HYPERTROPHIC OSTEOARTHROPATHY.肺性肥大性骨关节病
Arch Intern Med. 1963 Dec;112:947-53. doi: 10.1001/archinte.1963.03860060171019.
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HYPERTROPHIC PULMONARY OSTEOARTHROPATHY.肥厚性肺性骨关节病
J Thorac Cardiovasc Surg. 1963 Sep;46:310-21.
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Pulmonary hypertrophic osteoarthropathy.肺性肥大性骨关节病
Lancet. 1961 Dec 9;2(7215):1269-74. doi: 10.1016/s0140-6736(61)91138-2.
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Increased oestrogen excretion in hypertrophic pulmonary osteoarthropathy.肥厚性肺性骨关节病中雌激素排泄增加。
Lancet. 1961 Dec 9;2(7215):1274-6. doi: 10.1016/s0140-6736(61)91139-4.
10
Diffuse pleural mesothelioma and asbestos exposure in the North Western Cape Province.西开普省的弥漫性胸膜间皮瘤与石棉暴露
Br J Ind Med. 1960 Oct;17(4):260-71. doi: 10.1136/oem.17.4.260.