Waag K L, Joppich I, Brands W, Manegold B C
Klin Padiatr. 1979 Jan;191(1):78-82.
The congenital choledochus cyst is an extremely rare disease pattern. The author presents two own cases of boys aged 4 1/2 years in whom the disease was manifested as a fusiform dilatation of the cholodochus and of the other bile ducts on the one hand, and by a cyst in the second case. Both cases were characterised by an additional annular stenosis of the cholodochus immediately before the junction of the pancreatic duct. The article discusses the most essential criteria in respect of clinic, diagnosis and therapy, as well as the etiological aspects.
先天性胆总管囊肿是一种极为罕见的疾病类型。作者介绍了两例自己遇到的病例，患儿均为4岁半的男孩，一例表现为胆总管及其他胆管呈梭形扩张，另一例表现为囊肿。两例均有一个重要特征，即在胰管汇合处之前胆总管有一个额外的环形狭窄。本文讨论了关于临床、诊断、治疗以及病因方面的最基本标准。
