Miyakubo H, Hashimoto K, Miyakubo S
Ophthalmology. 1984 Dec;91(12):1524-30. doi: 10.1016/s0161-6420(84)34119-7.
We evaluated the retinal vascular pattern in 133 eyes (77 cases) with familial exudative vitreoretinopathy (FEVR). A wide variety of retinal vascular abnormalities were observed in the extreme fundus periphery, particularly in the temporal retinal sector. They included: presence of an avascular zone in the extreme periphery, vasodilation and arteriovenous anastomosis in the peripheral vascularized retina, v-shaped avascular zone along the temporal meridian, and neovascularization. A grading system into five types was proposed with these features as parameters. Macular ectopia, falciform retinal fold and vitreoretinal adhesion appeared to be secondary to retinal vascular abnormalities. The presence of sporadic FEVR is postulated.
我们评估了133只眼（77例）家族性渗出性玻璃体视网膜病变（FEVR）的视网膜血管形态。在眼底极周边部观察到多种视网膜血管异常，尤其是在颞侧视网膜区域。这些异常包括：极周边部无血管区的存在、周边血管化视网膜的血管扩张和动静脉吻合、沿颞侧子午线的V形无血管区以及新生血管形成。以这些特征为参数，提出了一个分为五种类型的分级系统。黄斑异位、镰状视网膜皱褶和玻璃体视网膜粘连似乎是视网膜血管异常的继发表现。推测存在散发性FEVR。
