Wexler H A, Dapena M V
Radiology. 1978 Mar;126(3):737-41. doi: 10.1148/126.3.737.
Most children with congenital cystic adenomatoid malformation present in the first six months of life. Three cases are described with unusually late presentation. One child was completely asymptomatic and another became symptomatic only after secondary infection of a congenital cystic adenomatoid malformation. In two cases the correct diagnosis was not made preoperatively. The value of preoperative lung scanning was demonstrated in one case in which a lung scan showed a larger perfused area than indicated on the radiograph. At operation, a lobulated cystic structure was seen attached by a thin pedicle to the interior surface of the left upper lobe.
大多数先天性囊性腺瘤样畸形患儿在出生后的头六个月内出现症状。本文描述了三例出现异常延迟表现的病例。一名患儿完全无症状，另一名患儿仅在先天性囊性腺瘤样畸形继发感染后才出现症状。在两例病例中，术前未做出正确诊断。术前肺部扫描的价值在一例病例中得到了证明，该例肺部扫描显示灌注区域比X光片所示的更大。手术时，可见一个分叶状的囊性结构通过细蒂附着于左上叶内表面。
