Pardini S, Laborde F, de Riberolles C, Leca F, Hazan E, Neveux J Y
Sem Hop. 1983 Jan 20;59(3):176-8.
Complete atrioventricular canal with tetralogy of Fallot is a rare occurrence (8%). Diagnosis rests on the association with Down syndrome and on data from EKG, ultrasonography and angiography. The high operative risk explains why radical surgery is done at an older age (9 years) than in the usual form of complete atrioventricular canal without associated anomalies (33 months) and why antecedent surgical palliation with anastomotic procedures is so frequent (68% of the cases reported in the medical literature). The same surgical procedure was done in all patients: closure of the defects with two separate patches lined with pericardium, suture of the mitral cleft and relief of the infundibular and pulmonary obstruction without valvulation.
完全性房室通道合并法洛四联症较为罕见(8%)。诊断依赖于与唐氏综合征的关联以及心电图、超声心动图和血管造影的数据。手术风险高解释了为什么根治性手术的实施年龄(9岁)比无相关异常的普通完全性房室通道(33个月)要大,也解释了为什么先行吻合术进行手术姑息治疗如此频繁(医学文献报道的病例中有68%)。所有患者均采用相同的手术方法:用两片心包衬里的单独补片封闭缺损,缝合二尖瓣裂,并解除漏斗部和肺动脉梗阻,不进行瓣膜成形术。