Tsuji S, Kuroiwa Y
Neurology. 1983 Nov;33(11):1503-6. doi: 10.1212/wnl.33.11.1503.
In a nationwide survey of Creutzfeldt-Jakob disease (CJD) in Japan, the point prevalence rate on June 1, 1978 in Fukuoka Prefecture and the estimated national prevalence rate were approximately one per one million population. The minimal period prevalence rate was 0.45 per one million population. The minimal annual incidence and the minimal annual mortality rate were 0.19 and 0.15 per one million population, respectively. The geographic distribution of CJD in Japan was uniform. Clinically, CJD affected the central nervous system diffusely and was rapidly fatal. No specific features were found in family, social, and past histories.
在一项针对日本克雅氏病（CJD）的全国性调查中，1978年6月1日福冈县的点患病率及估计的全国患病率约为每百万人口1例。最低时期患病率为每百万人口0.45例。最低年发病率和最低年死亡率分别为每百万人口0.19例和0.15例。日本CJD的地理分布是均匀的。临床上，CJD广泛影响中枢神经系统且迅速致命。在家族史、社会史和既往史中未发现特定特征。
