Bakhshi A, Minowada J, Arnold A, Cossman J, Jensen J P, Whang-Peng J, Waldmann T A, Korsmeyer S J
N Engl J Med. 1983 Oct 6;309(14):826-31. doi: 10.1056/NEJM198310063091404.
The origin and stage of differentiation of the blast-crisis cells in chronic myelogenous leukemia have remained uncertain. Because immunoglobulin heavy-chain and light-chain genes must undergo a DNA rearrangement during B-cell development but rarely do so in human non-B-cell lineages, we examined these genes in 18 episodes of chronic myelogenous leukemia. In eight of nine episodes of lymphoid blast crisis, heavy-chain genes were rearranged, and in three, rearrangements in light-chain genes were also present. In contrast, cells from chronic myeloid, myeloid blast, and erythroid-like phases retained germ-like immunoglobulin genes. The observed phenotypic markers and gene configurations revealed that most lymphoid blast crises represent stages of development of B-cell precursors. In two separate episodes of lymphoid crisis, cells from a single patient possessed identical heavy-chain but different light-chain-gene configurations. Thus, the precursor cells that monoclonally expand to produce a lymphoid crisis are capable of immunoglobulin-gene rearrangements and represent discrete steps in early B-cell maturation.
慢性粒细胞白血病原始细胞危象细胞的起源和分化阶段一直不确定。由于免疫球蛋白重链和轻链基因在B细胞发育过程中必须经历DNA重排,但在人类非B细胞谱系中很少发生,我们在18例慢性粒细胞白血病中检测了这些基因。在9例淋巴母细胞危象中的8例中,重链基因发生了重排,在3例中,轻链基因也存在重排。相比之下,慢性粒细胞期、髓母细胞期和类红细胞期的细胞保留了胚系免疫球蛋白基因。观察到的表型标记和基因构型表明,大多数淋巴母细胞危象代表B细胞前体的发育阶段。在两例独立的淋巴危象中,来自同一患者的细胞具有相同的重链但不同的轻链基因构型。因此,单克隆扩增产生淋巴危象的前体细胞能够进行免疫球蛋白基因重排,代表早期B细胞成熟的不同阶段。