Matsui T, Kuroda S, Mizutani M, Kiuchi Y, Suzuki K, Ono T
Vet Pathol. 1983 May;20(3):312-21. doi: 10.1177/030098588302000307.
Two Japanese quail which were incapable of wing movement and three normal quail were examined by histological and ultrastructural methods. The diseased birds had glycogen deposits in their skeletal muscle, cardiac muscle, smooth muscle, and nerve cells of the brain and spinal cord. According to the distribution of the lesions and the characteristics of the deposited glycogen, the diseased birds had glycogenosis which was analogous to type II found in man. The usefulness of this disease as a model for glycogenosis in man is discussed.
对两只无法进行翅膀运动的日本鹌鹑和三只正常鹌鹑进行了组织学和超微结构检查。患病鹌鹑的骨骼肌、心肌、平滑肌以及脑和脊髓的神经细胞中存在糖原沉积。根据病变分布和沉积糖原的特征,患病鹌鹑患有糖原贮积病,类似于人类发现的II型糖原贮积病。讨论了这种疾病作为人类糖原贮积病模型的实用性。